Functional domains of the SYT and SYT-SSX synovial sarcoma translocation proteins and co-localization with the SNF protein BRM in the nucleus

Hum Mol Genet. 1999 Apr;8(4):585-91. doi: 10.1093/hmg/8.4.585.

Abstract

The t(X;18)(p11.2;q11.2) chromosomal translocation commonly found in synovial sarcomas fuses the SYT gene on chromosome 18 to either of two similar genes, SSX1 or SSX2, on the X chromosome. The SYT protein appears to act as a transcriptional co-activator and the SSX proteins as co-repressors. Here we have investigated the functional domains of the proteins. The SYT protein has a novel conserved 54 amino acid domain at the N-terminus of the protein (the SNH domain) which is found in proteins from a wide variety of species, and a C-terminal domain, rich in glutamine, proline, glycine and tyrosine (the QPGY domain), which contains the transcriptional activator sequences. Deletion of the SNH domain results in a more active transcriptional activator, suggesting that this domain acts as an inhibitor of the activation domain. The C-terminal SSX domain present in SYT-SSX translocation protein contributes a transcriptional repressor domain to the protein. Thus, the fusion protein has transcriptional activating and repressing domains. We demonstrate that the human homologue of the SNF2/Brahama protein BRM co-localizes with SYT and SYT-SSX in nuclear speckles, and also interacts with SYT and SYT-SSX proteins in vitro. This interaction may provide an explanation of how the SYT protein activates gene transcription.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Binding Sites
  • Cell Nucleus / chemistry*
  • DNA Helicases
  • DNA-Binding Proteins / analysis
  • Green Fluorescent Proteins
  • Humans
  • Luminescent Proteins / genetics
  • Molecular Sequence Data
  • Neoplasm Proteins / genetics
  • Nuclear Proteins*
  • Oncogene Proteins, Fusion / analysis*
  • Oncogene Proteins, Fusion / genetics
  • Protein Binding
  • Proteins / analysis*
  • Proteins / genetics
  • Proteins / metabolism
  • Proto-Oncogene Proteins
  • Recombinant Fusion Proteins / analysis
  • Recombinant Fusion Proteins / genetics
  • Repressor Proteins / genetics
  • Sarcoma, Synovial / genetics*
  • Sequence Homology, Amino Acid
  • Transcription Factors / analysis*
  • Transcription Factors / metabolism
  • Transcriptional Activation
  • Translocation, Genetic

Substances

  • DNA-Binding Proteins
  • Luminescent Proteins
  • Neoplasm Proteins
  • Nuclear Proteins
  • Oncogene Proteins, Fusion
  • Proteins
  • Proto-Oncogene Proteins
  • Recombinant Fusion Proteins
  • Repressor Proteins
  • SMARCA2 protein, human
  • SS18 protein, human
  • Transcription Factors
  • Green Fluorescent Proteins
  • synovial sarcoma X breakpoint proteins
  • SMARCA4 protein, human
  • DNA Helicases