A rapid method for haemophilia B mutation detection using conformation sensitive gel electrophoresis

Br J Haematol. 1999 Mar;104(4):915-8. doi: 10.1046/j.1365-2141.1999.01274.x.

Abstract

Conformation sensitive gel electrophoresis (CSGE) was confirmed as an effective procedure for screening the factor IX (FIX) gene by detecting 10/10 previously known FIX gene mutations. The FIX genes of a further 11 haemophilia B patients with unknown mutations were then screened and an abnormal CSGE profile was identified in all cases. Subsequent DNA sequencing demonstrated one of these to be a novel mutation (31133insT, Arg338Fs), the remaining 10 having been previously reported on the haemophilia B database. Mutation screening of the FIX gene using CSGE was demonstrated to be a rapid and efficient means of carrier analysis in families with haemophilia B.

MeSH terms

  • Electrophoresis, Agar Gel / methods
  • Factor IX / genetics*
  • Female
  • Genetic Carrier Screening / methods*
  • Hemophilia B / diagnosis
  • Hemophilia B / genetics*
  • Humans
  • Male
  • Mutation / genetics*
  • Sensitivity and Specificity

Substances

  • Factor IX