MPS II in females: molecular basis of two different cases

J Med Genet. 2000 Oct;37(10):E29. doi: 10.1136/jmg.37.10.e29.
No abstract available

Publication types

  • Case Reports
  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alleles
  • Animals
  • Blotting, Southern
  • Cell Line
  • Child
  • Child, Preschool
  • Chromosome Deletion*
  • DNA Methylation
  • Dosage Compensation, Genetic*
  • Fatal Outcome
  • Female
  • Fibroblasts
  • France
  • Genes, Recessive / genetics
  • Humans
  • Hybrid Cells / drug effects
  • Hybrid Cells / enzymology
  • Hybrid Cells / metabolism
  • Iduronate Sulfatase / genetics*
  • Iduronate Sulfatase / metabolism
  • In Situ Hybridization, Fluorescence
  • Introns / genetics
  • Male
  • Mucopolysaccharidosis II / enzymology
  • Mucopolysaccharidosis II / genetics*
  • Mutation / genetics*
  • Ouabain / pharmacology
  • Phenotype
  • Polymorphism, Genetic / genetics
  • RNA, Messenger / analysis
  • RNA, Messenger / genetics
  • X Chromosome / genetics*

Substances

  • RNA, Messenger
  • Ouabain
  • Iduronate Sulfatase