Functional association of the parkin gene promoter with idiopathic Parkinson's disease

Hum Mol Genet. 2002 Oct 15;11(22):2787-92. doi: 10.1093/hmg/11.22.2787.

Abstract

Loss-of-function mutations in the parkin gene were first identified in autosomal recessive juvenile parkinsonism (AR-JP). Subsequently, parkin mutations were found in many early-onset patients with Parkinson's disease (PD) (<45 years at onset). We hypothesized that parkin gene expression also may contribute to the age-associated risk of idiopathic PD (>50 years at onset). Two single-nucleotide polymorphisms within the parkin core promoter have been identified and assessed. We show one of the variants, -258 T/G, is located in a region of DNA that binds nuclear protein from human substantia nigra in vitro and functionally affects gene transcription. Furthermore, the -258 T/G polymorphism is genetically associated with idiopathic PD, as assessed in a large population-based series of cases and controls. Our results further implicate the parkin gene in the development of Parkinson's disease.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Aged
  • Base Sequence
  • Binding Sites / genetics
  • Case-Control Studies
  • Cell Line
  • DNA / genetics
  • DNA / metabolism
  • Humans
  • In Vitro Techniques
  • Ligases / genetics*
  • Molecular Sequence Data
  • Mutation
  • Nerve Tissue Proteins / metabolism
  • Nuclear Proteins / metabolism
  • Parkinson Disease / genetics*
  • Parkinson Disease / metabolism
  • Polymorphism, Single Nucleotide
  • Promoter Regions, Genetic*
  • Substantia Nigra / metabolism
  • Transfection
  • Ubiquitin-Protein Ligases*

Substances

  • Nerve Tissue Proteins
  • Nuclear Proteins
  • DNA
  • Ubiquitin-Protein Ligases
  • parkin protein
  • Ligases