Prenatal diagnosis of Werdnig-Hoffmann disease in China

Chin Med J (Engl). 2003 May;116(5):673-5.

Abstract

Objective: To establish a means for prenatal prediction of spinal muscular atrophy (SMA) through survival motor neuron (SMN) gene deletion analysis and genetic counseling in families with a child affected with SMA.

Methods: Genetic analysis for prenatal prediction of Werdnig-Hoffmann disease was performed in a at risk Chinese family by polymerase chain reaction (PCR)-single-strand conformation polymorphism (SSCP) in SMN gene exons 7 and 8.

Results: The pregnancy was positive for the homozygous deletion of the SMN gene, thus the fetus was diagnosed as being affected and the pregnancy was terminated.

Conclusion: This approach is fast and reliable for DNA-based prenatal diagnosis of Werdnig-Hoffmann disease.

Publication types

  • Case Reports

MeSH terms

  • China
  • Female
  • Fetal Diseases / diagnosis*
  • Gene Deletion
  • Genetic Counseling
  • Humans
  • Pregnancy
  • Prenatal Diagnosis*
  • Spinal Muscular Atrophies of Childhood / diagnosis*
  • Spinal Muscular Atrophies of Childhood / genetics