Pael-R is accumulated in Lewy bodies of Parkinson's disease

Ann Neurol. 2004 Mar;55(3):439-42. doi: 10.1002/ana.20064.

Abstract

We examined the distribution of Pael-R, a newly identified substrate for Parkin, in Parkinson's disease (PD) and multiple system atrophy (MSA). Pael-R, Parkin, alpha-synuclein, and ubiquitin accumulated in Lewy bodies (LBs) and neurites. Pael-R was localized in the core of LBs. Parkin and alpha-synuclein accumulated in the halo, neuronal cell bodies, and processes. These findings potentially suggest the involvement of Pael-R in LB formation, and protection role of Parkin in Pael-R-mediated neurotoxicity in PD. The absence of Pael-R and Parkin in glial cytoplasmic inclusions (GCIs) in MSA implies a distinct pathway involved in the formation of LBs and GCIs.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Aged, 80 and over
  • Brain / cytology
  • Brain / metabolism
  • Female
  • Humans
  • Immunohistochemistry / methods
  • Lewy Bodies / metabolism*
  • Male
  • Middle Aged
  • Multiple System Atrophy / metabolism
  • Nerve Tissue Proteins / metabolism
  • Neurites / metabolism
  • Neurons / metabolism
  • Parkinson Disease / metabolism*
  • Receptors, G-Protein-Coupled / metabolism*
  • Synucleins
  • Ubiquitin / metabolism
  • Ubiquitin-Protein Ligases / metabolism
  • alpha-Synuclein

Substances

  • GPR37 receptor, human
  • Nerve Tissue Proteins
  • Receptors, G-Protein-Coupled
  • SNCA protein, human
  • Synucleins
  • Ubiquitin
  • alpha-Synuclein
  • Ubiquitin-Protein Ligases
  • parkin protein