Medium chain acyl-coenzyme A dehydrogenase deficiency and SIDS

T Hegyi; B Ostfeld; K Gardner

Medium chain acyl-coenzyme A dehydrogenase deficiency and SIDS

N J Med. 1992 May;89(5):385-92.

Authors

T Hegyi¹, B Ostfeld, K Gardner

Affiliation

¹ Division of Neonatology, St. Peter's Medical Center, UMDNJ-Robert Wood Johnson Medical School, New Brunswick 08903.

PMID: 1635678

Abstract

Medium chain acyl-coenzyme A dehydrogenase deficiency (MCADD) is a potentially fatal genetic defect in fatty acid metabolism and may account for a proportion of all deaths initially attributed to sudden infant death syndrome (SIDS). Effective therapy and prevention are available.

Publication types

Review

MeSH terms

Acyl-CoA Dehydrogenase
Dietary Fats / administration & dosage
Fatty Acid Desaturases / deficiency*
Fatty Acids, Nonesterified / metabolism*
Food, Formulated
Humans
Infant
Milk, Human / chemistry
Sudden Infant Death / etiology*

Substances

Dietary Fats
Fatty Acids, Nonesterified
Fatty Acid Desaturases
Acyl-CoA Dehydrogenase