Anesthetic management of a patient with Gerstmann-Sträussler-Scheinker syndrome (mutation of prion protein)

Anesth Analg. 2006 Apr;102(4):1285-6. doi: 10.1213/01.ane.0000198630.65752.c9.

Abstract

Gerstmann-Sträussler-Scheinker Syndrome (GSS) is a rare, infectious syndrome related to a mutation in the prion protein. A 60-yr-old, 152-cm, 31-kg woman with GSS was scheduled for open gastrostomy. This is the first report about an anesthetic experience in a patient with GSS. We describe our experience and precautions in the anesthetic management of a GSS patient.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Airway Obstruction / prevention & control
  • Anesthesia / methods*
  • Equipment Contamination / prevention & control
  • Female
  • Gerstmann-Straussler-Scheinker Disease / genetics
  • Gerstmann-Straussler-Scheinker Disease / surgery*
  • Humans
  • Intubation, Intratracheal / instrumentation
  • Intubation, Intratracheal / methods
  • Middle Aged
  • Mutation / genetics*
  • Prions / genetics*

Substances

  • Prions