Juvenile dermatomyositis presenting with periorbital edema

Ophthalmic Plast Reconstr Surg. 2006 Sep-Oct;22(5):393-5. doi: 10.1097/01.iop.0000230271.21976.0d.

Abstract

Juvenile dermatomyositis is a rare disease that affects the skin and muscles. It often presents with a classic heliotrope eyelid rash. We present a case of juvenile dermatomyositis presenting with significant bilateral periorbital edema, with its complete resolution after systemic antiinflammatory therapy.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Biopsy
  • Dermatomyositis / complications*
  • Dermatomyositis / diagnosis
  • Dermatomyositis / drug therapy
  • Diagnosis, Differential
  • Edema / diagnosis
  • Edema / drug therapy
  • Edema / etiology*
  • Follow-Up Studies
  • Glucocorticoids / therapeutic use
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Orbital Diseases / diagnosis
  • Orbital Diseases / drug therapy
  • Orbital Diseases / etiology*

Substances

  • Glucocorticoids