Restoration of radiation resistance in ataxia telangiectasia cells by the introduction of normal human chromosome 11

Mutat Res. 1990 Mar;235(2):59-63. doi: 10.1016/0921-8777(90)90058-d.

Abstract

In order to identify the human chromosome which carries a mutated gene in cells from a patient with the hereditary disorder ataxia telangiectasia belonging to complementation group D (AT-D), we performed chromosome transfer experiments via microcell fusion. A single, pSV2neo-tagged chromosome, either 11 or 12, derived from normal human fibroblasts was introduced into AT-D cells by microcell fusion, and clones which were resistant to the antibiotic G418 were isolated. All 3 hybrid clones containing an additional copy number of chromosome 11 showed a restoration of the resistance of wild-type cells to killing by X-irradiation, whereas all 3 hybrid clones containing an additional copy number of chromosome 12 remained hyper-radiosensitive, like the parental AT cells. The results indicate that a defective gene of AT-D cells is also located on chromosome 11, since a genetic linkage analysis has previously suggested that a defective gene of its complementation group A is located on this chromosome.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Ataxia Telangiectasia / genetics*
  • Ataxia Telangiectasia / immunology
  • Cell Line, Transformed
  • Cell Transformation, Viral
  • Chromosomes, Human, Pair 11*
  • Chromosomes, Human, Pair 12
  • Humans
  • Hybrid Cells
  • Nuclear Transfer Techniques
  • Radiation Tolerance / genetics*
  • Simian virus 40