Hyperphagia among patients with Bardet-Biedl syndrome

Pediatr Obes. 2013 Oct;8(5):e64-7. doi: 10.1111/j.2047-6310.2013.00182.x. Epub 2013 Jun 18.

Abstract

Background: The importance of hyperphagia as a cause for energy imbalance in humans with Bardet-Biedl syndrome (BBS) has not been established. We therefore compared hyperphagic symptoms in patients with BBS vs. controls.

Methods: We studied 13 patients with BBS and 23 non-syndromic controls with similar age, sex and body mass index (BMI) z-score. A 13-item hyperphagia questionnaire was completed by patients' parents/guardians.

Results: Total hyperphagia questionnaire score was higher in BBS than controls (27.6 ± 9.0 vs. 19.1 ± 7.9, P = 0.005). Behaviour and drive subscales were higher for BBS than controls (12.5 ± 4.1 vs. 7.8 ± 3.2, P = 0.001, and 11.2 ± 4.1 vs. 8.3 ± 3.8, P = 0.04, respectively); severity was not significantly different between groups (3.8 ± 1.5 vs. 3.0 ± 1.3, P = 0.072). After adjustment for demographic variables and BMI z-score, total and behaviour subscale scores remained significantly different between groups, suggesting food-seeking activity, rather than preoccupation with food may be the main hyperphagic feature among patients with BBS.

Conclusion: Appetite dysregulation may contribute to obesity in BBS.

Keywords: Bardet-Biedl syndrome; hyperphagia; obesity syndromes; polyphagia.

Publication types

  • Comparative Study
  • Research Support, N.I.H., Extramural

MeSH terms

  • Age of Onset
  • Bardet-Biedl Syndrome / complications*
  • Bardet-Biedl Syndrome / metabolism
  • Bardet-Biedl Syndrome / psychology
  • Body Composition
  • Body Mass Index
  • Child
  • Energy Metabolism
  • Female
  • Humans
  • Hyperphagia / complications*
  • Hyperphagia / metabolism
  • Hyperphagia / psychology
  • Male
  • Obesity / etiology*
  • Obesity / metabolism
  • Obesity / psychology
  • Parents
  • Surveys and Questionnaires