Abstract
Four patients in a family with punctate palmoplantar keratoderma (Buschke-Fischer) associated with Morbus Bechterew and HLA B 27 in 3 of the family members are reported. Without severe side effect, the proband was successfully treated with 50 mg etretinate per day for 6 weeks.
MeSH terms
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Adolescent
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Adult
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Female
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HLA-B Antigens / analysis
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HLA-B Antigens / genetics*
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HLA-B27 Antigen
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Humans
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Keratoderma, Palmoplantar / complications
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Keratoderma, Palmoplantar / immunology
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Male
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Middle Aged
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Pedigree
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Spondylitis, Ankylosing / complications
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Spondylitis, Ankylosing / immunology
Substances
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HLA-B Antigens
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HLA-B27 Antigen