Abstract
Surgical correction of patients with tetralogy of Fallot with pulmonary atresia is now one of the routine procedures performed by pediatric cardiac surgeons. In one variant, the pulmonary arterial supply is derived from a fistulous communication from the coronary arteries. This rare and interesting situation poses a diagnostic and therapeutic dilemma, as well as providing specific management challenges to the surgical team. Here, we discuss important aspects of this rare variant, specifically its morphology, presentation, evaluation and management.
Keywords:
Arterio-arterial fistula; congenital; fistula; heart defects; pulmonary atresia; tetralogy of Fallot.
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MeSH terms
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Arterio-Arterial Fistula / complications*
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Arterio-Arterial Fistula / diagnosis
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Arterio-Arterial Fistula / physiopathology
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Arterio-Arterial Fistula / surgery
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Coronary Angiography / methods
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Coronary Circulation
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Coronary Vessel Anomalies / complications*
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Coronary Vessel Anomalies / diagnosis
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Coronary Vessel Anomalies / physiopathology
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Coronary Vessel Anomalies / surgery
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Hemodynamics
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Humans
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Predictive Value of Tests
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Pulmonary Artery / abnormalities*
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Pulmonary Artery / diagnostic imaging
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Pulmonary Artery / physiopathology
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Pulmonary Artery / surgery
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Pulmonary Atresia / complications*
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Pulmonary Atresia / diagnosis
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Pulmonary Atresia / physiopathology
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Pulmonary Atresia / surgery
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Pulmonary Circulation
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Tetralogy of Fallot / complications*
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Tetralogy of Fallot / diagnosis
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Tetralogy of Fallot / physiopathology
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Tetralogy of Fallot / surgery
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Tomography, X-Ray Computed
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Treatment Outcome