Introduction: Lymphangioma is a rare benign cyst caused by congenital malformation of the lymphatic systems that often occurs in the cervicofacial region. There is no consensus on its management: Observation, aspiration, injection, cryotherapy, electrocautery, radiation, laser, ligation and excision.
Methods: We performed a literature search with the keywords "cystic hygroma", "lymphangioma", "management", "OK 432" and "picibanil" from Medline, Embase and PubMed databases.
Results: We present a review of the history, signs and symptoms, diagnosis, histology, classification and management options of cystic hygroma.
Conclusion: There is no consensus on the treatment options. It should be individualised depending on the size of the lesion, anatomic localisation and complications.