Tetralogy of Fallot: General Principles of Management

Tacy E Downing; Yuli Y Kim

doi:10.1016/j.ccl.2015.07.002

Tetralogy of Fallot: General Principles of Management

Cardiol Clin. 2015 Nov;33(4):531-41, vii-viii. doi: 10.1016/j.ccl.2015.07.002. Epub 2015 Aug 29.

Authors

Tacy E Downing¹, Yuli Y Kim²

Affiliations

¹ Division of Cardiology, The Children's Hospital of Philadelphia, Suite 8NW90, 3400 Civic Center Boulevard, Philadelphia, PA 19104, USA.
² Division of Cardiovascular Medicine, The Hospital of the University of Pennsylvania, Perelman School of Medicine at the University of Pennsylvania, 3400 Civic Center Boulevard, Philadelphia, PA 19104, USA; Philadelphia Adult Congenital Heart Center, The Children's Hospital of Philadelphia, Perelman Center for Advanced Medicine, Penn Medicine, 3400 Civic Center Boulevard, 2nd Floor East Pavilion, Philadelphia, PA 19104, USA. Electronic address: Yuli.Kim@uphs.upenn.edu.

PMID: 26471818
DOI: 10.1016/j.ccl.2015.07.002

Abstract

Repaired tetralogy of Fallot (TOF) is one of the most common diagnoses encountered when caring for adults with congenital heart disease. Although long-term survival after childhood TOF repair is excellent, morbidity is common and most patients require reintervention in adulthood. This review provides an overview of key surveillance and management issues for adults with TOF, including residual right ventricular outflow tract disease and timing of pulmonary valve replacement, arrhythmias and risk stratification, left-sided heart disease and heart failure, and pregnancy management.

Keywords: Adults with congenital heart disease; Arrhythmia; Pregnancy; Pulmonary regurgitation; Pulmonary valve replacement; Tetralogy of Fallot.

Publication types

Review

MeSH terms

Adult
Disease Management*
Female
Humans
Male
Patient Selection
Practice Guidelines as Topic
Pregnancy
Tetralogy of Fallot / complications
Tetralogy of Fallot / diagnosis*
Tetralogy of Fallot / surgery*