Hb Dapu (HBA2: c.52G > T): A Novel Nondeletional α-Thalassemia Mutation

Hemoglobin. 2016 Aug;40(4):264-6. doi: 10.1080/03630269.2016.1187164. Epub 2016 Jun 3.

Abstract

We report a novel mutation on the α2-globin gene, Hb Dapu [α17(A15)Val →Phe (α2); HBA2: c.52G > T] detected in a Chinese family. This mutation gives rise to a previously undescribed hemoglobin (Hb) variant that was undetectable by electrophoretic or chromatographic methods. The combination of this mutation with an in cis deletion of a double α-globin gene resulting in a mild form of Hb H (β4) disease, is consistent with a thalassemic phenotype associated with the novel mutation.

Keywords: Hb Dapu; nondeletional mutation; α-thalassemia (α-thal); α2-globin gene.

MeSH terms

  • Asian People
  • Hemoglobin A2 / genetics*
  • Hemoglobins, Abnormal / genetics*
  • Humans
  • Phenotype
  • Point Mutation
  • Sequence Deletion
  • alpha-Globins / genetics
  • alpha-Thalassemia / genetics*

Substances

  • Hemoglobins, Abnormal
  • alpha-Globins
  • Hemoglobin A2