Right Ventricular Outflow Tract Obstruction: Pulmonary Atresia With Intact Ventricular Septum, Pulmonary Stenosis, and Ebstein's Malformation

David M Kwiatkowski; Frank L Hanley; Catherine D Krawczeski

doi:10.1097/PCC.0000000000000818

Right Ventricular Outflow Tract Obstruction: Pulmonary Atresia With Intact Ventricular Septum, Pulmonary Stenosis, and Ebstein's Malformation

Pediatr Crit Care Med. 2016 Aug;17(8 Suppl 1):S323-9. doi: 10.1097/PCC.0000000000000818.

Authors

David M Kwiatkowski¹, Frank L Hanley, Catherine D Krawczeski

Affiliation

¹ 1Department of Pediatrics, Section of Cardiology, Stanford University School of Medicine, Lucile Packard Children's Hospital, Palo Alto, CA. 2Department of Surgery, Chief, Pediatric Cardiac Surgery, Stanford University School of Medicine, Lucile Packard Children's Hospital, Palo Alto, CA. 3Department of Pediatrics, Section of Cardiology, Stanford University School of Medicine, Cardiac Intensive Care Unit, Lucile Packard Children's Hospital, Palo Alto, CA.

PMID: 27490618
DOI: 10.1097/PCC.0000000000000818

Abstract

Objectives: The objectives of this review are to discuss the anatomy, pathophysiology, clinical course, and current treatment strategies for pulmonary atresia with intact ventricular septum, pulmonary stenosis, and Ebstein's anomaly.

Data source: MEDLINE and PubMed.

Conclusions: Considerable advances have been made in management strategies for these complex congenital heart lesions, which have led to improved outcomes.

Publication types

Review

MeSH terms

Cardiac Surgical Procedures / adverse effects
Cardiac Surgical Procedures / methods*
Ebstein Anomaly / complications
Ebstein Anomaly / surgery*
Heart Defects, Congenital / complications
Heart Defects, Congenital / surgery*
Humans
Infant, Newborn
Pulmonary Atresia / complications
Pulmonary Atresia / surgery*
Pulmonary Valve Stenosis / complications
Pulmonary Valve Stenosis / surgery*
Ventricular Outflow Obstruction / surgery*

Supplementary concepts

Pulmonary Atresia with Intact Ventricular Septum