Abstract
Ivemark syndrome or right atrial isomerism is a rare syndrome of asplenia / hyposplenia with malformation of heart and abnormal arrangement of internal organs of chest and abdomen and is classified under heterotaxy disorder. We describe here the case of a 14 year old boy diagnosed with asplenia, dextrocardia with double outlet right ventricle and midline liver.
© Journal of the Association of Physicians of India 2011.
MeSH terms
-
Abnormalities, Multiple / diagnosis
-
Abnormalities, Multiple / diagnostic imaging*
-
Adolescent
-
Bronchiectasis / diagnostic imaging*
-
Dextrocardia / diagnostic imaging*
-
Double Outlet Right Ventricle / diagnostic imaging*
-
Heart Defects, Congenital / diagnosis
-
Heart Defects, Congenital / diagnostic imaging*
-
Heterotaxy Syndrome / diagnosis*
-
Heterotaxy Syndrome / physiopathology
-
Humans
-
Liver / abnormalities*
-
Male
-
Tomography, X-Ray Computed
-
Transposition of Great Vessels / diagnostic imaging