Asymptomatic Interrupted Aortic Arch, Severe Tricuspid Regurgitation, and Bicuspid Aortic Valve in a 76-Year-Old Woman

Tex Heart Inst J. 2016 Oct 1;43(5):437-440. doi: 10.14503/THIJ-15-5320. eCollection 2016 Oct.

Abstract

Interrupted aortic arch is a rare congenital abnormality with a high infancy mortality rate. The principal finding is loss of luminal continuity between the ascending and descending portions of the aorta. Because of the high mortality rate in infancy, interrupted aortic arch is very rare among adults. In this report, we describe the case of a 76-year-old woman with asymptomatic interrupted aortic arch, severe tricuspid regurgitation, and bicuspid aortic valve. To our knowledge, she is the oldest patient ever reported with this possibly unique combination of pathologic conditions. In addition to reporting her case, we review the relevant medical literature.

Keywords: Adult; aorta, thoracic/abnormalities; aortic valve/abnormalities; arteriovenous malformations/diagnosis/surgery; heart defects, congenital; tricuspid valve/pathology; vascular malformations/physiopathology.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Abnormalities, Multiple*
  • Aged
  • Aorta, Thoracic / abnormalities*
  • Aorta, Thoracic / diagnostic imaging
  • Aorta, Thoracic / physiopathology
  • Aorta, Thoracic / surgery
  • Aortic Valve / abnormalities*
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / physiopathology
  • Aortography / methods
  • Bicuspid Aortic Valve Disease
  • Cardiac Surgical Procedures / adverse effects
  • Computed Tomography Angiography
  • Fatal Outcome
  • Female
  • Heart Valve Diseases / complications*
  • Heart Valve Diseases / diagnostic imaging
  • Heart Valve Diseases / physiopathology
  • Humans
  • Severity of Illness Index
  • Treatment Outcome
  • Tricuspid Valve Insufficiency / complications*
  • Tricuspid Valve Insufficiency / diagnostic imaging
  • Tricuspid Valve Insufficiency / physiopathology
  • Tricuspid Valve Insufficiency / surgery
  • Tricuspid Valve* / diagnostic imaging
  • Tricuspid Valve* / physiopathology
  • Tricuspid Valve* / surgery
  • Vascular Grafting / adverse effects