Treatment of Ribbing disease with 5-year follow-up and literature review

Osteoporos Int. 2017 Apr;28(4):1499-1502. doi: 10.1007/s00198-016-3896-9. Epub 2017 Jan 18.

Abstract

Ribbing disease, or multiple diaphyseal sclerosis, is a rare diaphyseal sclerosis of unknown etiology. Patients with this pathology usually present with asymmetric pain limited to the lower extremities. Though all efforts are made to relieve the progressive pain associated with Ribbing disease, no medical or surgical treatments have been established yet. In this case report, we followed up a Ribbing case with sclerotic bone fenestration for 5 years. The radiological changes and the clinical effects are described, and the different Ribbing treatments are then briefly reviewed.

Keywords: Bone fenestration; Ribbing disease.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Camurati-Engelmann Syndrome / complications
  • Camurati-Engelmann Syndrome / diagnostic imaging
  • Camurati-Engelmann Syndrome / surgery*
  • Female
  • Femur / surgery
  • Follow-Up Studies
  • Humans
  • Magnetic Resonance Imaging
  • Osteoma, Osteoid / complications
  • Osteoma, Osteoid / diagnostic imaging
  • Osteoma, Osteoid / surgery*
  • Pain / etiology
  • Radionuclide Imaging
  • Technetium Tc 99m Medronate
  • Tomography, X-Ray Computed

Substances

  • Technetium Tc 99m Medronate

Supplementary concepts

  • Ribbing disease