A rare cause of early neonatal cyanosis: absent right pulmonary artery

BMJ Case Rep. 2017 Aug 9:2017:bcr2017220978. doi: 10.1136/bcr-2017-220978.

Abstract

Unilateral absent right pulmonary artery is a rare developmental anomaly that usually presents in late childhood and adolescence as recurrent respiratory tract infections, dyspnoea and haemoptysis. We report a case of a 2-day-old baby with respiratory distress and differential cyanosis. Echocardiogram showed pulmonary hypertension with absent right pulmonary artery. The findings were confirmed by CT angiogram. The baby improved with pulmonary vasodilators and antifailure medications.

Keywords: Neonatal Health; Neonatal Intensive Care.

Publication types

  • Case Reports

MeSH terms

  • Computed Tomography Angiography
  • Cyanosis / etiology
  • Diagnosis, Differential
  • Echocardiography
  • Humans
  • Hypertension, Pulmonary / diagnosis*
  • Hypertension, Pulmonary / diagnostic imaging
  • Hypertension, Pulmonary / drug therapy
  • Infant, Newborn
  • Male
  • Pulmonary Artery / abnormalities*
  • Pulmonary Artery / diagnostic imaging
  • Respiratory System Abnormalities / diagnosis*
  • Respiratory System Abnormalities / diagnostic imaging
  • Sildenafil Citrate / administration & dosage
  • Sildenafil Citrate / therapeutic use
  • Vasodilator Agents / administration & dosage
  • Vasodilator Agents / therapeutic use

Substances

  • Vasodilator Agents
  • Sildenafil Citrate