Double-outlet left ventricle with a bicuspid pulmonary valve and aortic coarctation

J Clin Ultrasound. 2018 May;46(4):265-268. doi: 10.1002/jcu.22520. Epub 2017 Sep 7.

Abstract

A double-outlet left ventricle (DOLV) is a rare congenital cardiac malformation. Here, we describe a case of DOLV with bicuspid pulmonary valve, aortic coarctation, and a subpulmonary ventricular septal defect in which both ventricles were well developed. The anatomic features were observed with echocardiography, and the diagnosis was confirmed at surgery. Many variations of DOLV have been described. The features of our case expand the spectrum of this entity and may provide new insight into its complex anatomy.

Keywords: aortic coarctation; bicuspid pulmonary valve; double-outlet left ventricle; echocardiography; ventricular septal defect.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / diagnostic imaging*
  • Aortic Coarctation / diagnostic imaging*
  • Echocardiography*
  • Female
  • Heart Septal Defects, Ventricular / diagnostic imaging*
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Humans
  • Infant, Newborn
  • Pulmonary Valve / abnormalities*
  • Pulmonary Valve / diagnostic imaging