Nonsyndromic Craniosynostosis

Clin Plast Surg. 2019 Apr;46(2):123-139. doi: 10.1016/j.cps.2018.11.001. Epub 2019 Jan 30.

Abstract

Nonsyndromic craniosynostosis is significantly more common than syndromic craniosynostosis, affecting the sagittal, coronal, metopic, and lambdoid sutures in decreasing order of frequency. Nonsyndromic craniosynostosis is most frequently associated with only 1 fused suture, creating a predictable head shape. Repair of craniosynostosis is recommended to avoid potential neurodevelopmental delay. Early intervention at 3 to 4 months of age allows minimally invasive approaches, but requires postoperative molding helmet therapy and good family compliance. Open techniques are deferred until the child is older to better tolerate the associated surgical stress. Cranial vault remodeling is generally well-tolerated with a low rate of complications.

Keywords: Cranial suture; Cranial vault remodeling; Craniosynostosis; Nonsyndromic craniosynostosis; Pediatric craniofacial surgery.

Publication types

  • Review

MeSH terms

  • Cranial Sutures / abnormalities
  • Cranial Sutures / diagnostic imaging
  • Craniosynostoses / diagnostic imaging
  • Craniosynostoses / surgery*
  • Female
  • Head Protective Devices
  • Humans
  • Imaging, Three-Dimensional
  • Infant
  • Male
  • Osteotomy / methods*
  • Plastic Surgery Procedures / adverse effects
  • Plastic Surgery Procedures / methods*
  • Postoperative Care
  • Skull / diagnostic imaging
  • Skull / surgery*
  • Tomography, X-Ray Computed