Idiopathic intracranial hypertension is a rare disorder of elevated intracranial pressure with normal cerebrospinal fluid composition and without intracranial pathology. This condition primarily affects obese women of childbearing age and frequently causes headaches, vision loss, diplopia, tinnitus, and nausea. The incidence of idiopathic intracranial hypertension is rising along with obesity rates. Primary care and ED clinicians must recognize the signs and symptoms of idiopathic intracranial hypertension and intervene promptly to control symptoms and to preserve vision. This article reviews the clinical presentation and management of patients with idiopathic intracranial hypertension.