Paradigm Shift in the Management of Isolated Interrupted Aortic Arch in Adulthood

Curr Probl Cardiol. 2021 Mar;46(3):100717. doi: 10.1016/j.cpcardiol.2020.100717. Epub 2020 Sep 24.

Abstract

An interrupted aortic arch (IAA) is a rare type of congenital heart disease, and few patients survived into the adulthood. Surgical reconstruction is still the recommended approach, despite its complexity and considerable complication. In addition, patients with IAA usually suffer from several other important congenital heart anomalies, which increase the complexity of surgical management of IAA. Although endovascular therapy has replaced surgery in the treatment of the majority of non-IAA, its applicability in IAA is still matter of debate. In the present review, we have discussed about various therapeutic solutions of IAA, and present a stepwise approach for its endovascular management.

Publication types

  • Review

MeSH terms

  • Adult
  • Aorta, Thoracic* / diagnostic imaging
  • Aorta, Thoracic* / surgery
  • Heart Defects, Congenital* / diagnostic imaging
  • Heart Defects, Congenital* / surgery
  • Humans