Adolescent With von Willebrand Disease Type 3 Spontaneous Abdominal Hemorrhage

J Emerg Nurs. 2021 Jul;47(4):661-668. doi: 10.1016/j.jen.2021.04.008.

Abstract

An adolescent female classified as unstable with a spontaneous abdominal hemorrhage was transferred to a level 1 pediatric trauma tertiary emergency department. Pertinent medical history included von Willebrand disease type 3, menorrhagia, and obesity. Preparation before patient arrival included mobilization of multidisciplinary medical team experts in hematology, pharmacy, blood bank, radiology, and nursing who provided lifesaving interventions. The administration of factor products, blood products, interventional radiology, emergent hepatic angiography, and embolization coordination resulted in a successful outcome. After an 18-day intensive hospital course, the patient returned home close to her baseline health status.

Keywords: Humate-P; Vonvendi; von Willebrand disease type 3.

MeSH terms

  • Adolescent
  • Child
  • Female
  • Hemorrhage
  • Humans
  • von Willebrand Diseases* / complications
  • von Willebrand Diseases* / diagnosis
  • von Willebrand Diseases* / therapy