Treatment outcomes of hips in patients with epiphyseal dysplasia

J Pediatr Orthop B. 2022 Nov 1;31(6):554-559. doi: 10.1097/BPB.0000000000000982. Epub 2022 May 3.

Abstract

Hip containment surgeries in multiple epiphyseal and spondyloepiphyseal dysplasia (MED/SED) patients aim to improve the mechanical environment of the hip joint. The purpose of this study was to determine if surgical intervention to improve femoral head coverage improved radiographic and clinical outcomes. A retrospective study identified patients with MED/SED seen in clinic between May 2000 and September 2017, with a minimum of 2-year follow-up. Patient charts/radiographs were reviewed for radiographic hip measurements, pain, and gait. Sixty-nine hips in 35 patients were identified. Forty-four hips were treated nonoperatively and 25 were treated surgically. The mean age at diagnosis was 6.2 years. The mean follow-up was 7.7 years for the surgical group and 7.1 years for the nonsurgical group. The mean postoperative follow-up was 5.4 years. Acetabular index decreased from initial to final visit by 9.0° in the surgical group and 1.6° in the nonsurgical group. Tonnis angle decreased by 13.5° in the surgical group and 1.5° in the nonsurgical group. Center edge angle increased by 19.0° in the surgical group and 7.1° in the nonsurgical group. Hips in the surgical group were 6.1 times more likely to experience an improvement in pain compared with hips in the nonsurgical group. Gait at the final follow-up was similar among the two groups. In this study cohort, containment surgery provided increased femoral head coverage; however, there was equal femoral head deformation despite intervention. Hips treated surgically were more likely to experience an improvement in pain; however, gait alterations did not improve.

MeSH terms

  • Acetabulum / surgery
  • Child
  • Chronic Disease
  • Hip Joint / diagnostic imaging
  • Hip Joint / surgery
  • Humans
  • Musculoskeletal Abnormalities*
  • Osteochondrodysplasias* / diagnostic imaging
  • Osteochondrodysplasias* / surgery
  • Osteotomy / adverse effects
  • Pain / etiology
  • Retrospective Studies
  • Treatment Outcome