Essential thrombocythemia: a clonal disorder of hematopoietic stem cell

Am J Hematol. 1983 Apr;14(2):193-6. doi: 10.1002/ajh.2830140212.

Abstract

We studied 5 patients with essential thrombocythemia utilizing glucose-6-phosphate dehydrogenase (G-6-PD) enzyme as a cell marker for determining clonality. One of the patients was found to be heterozygous for isoenzymes B and A in the nonhaemopoietic tissues such as fibroblasts, but manifested only isoenzyme type B in the erythrocytes, neutrophils, and platelets. Our studies support the concept that essential thrombocythemia is a clonal disorder arising in a multipotent stem cell.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Blood Platelets / enzymology
  • Clone Cells / enzymology
  • Clone Cells / pathology*
  • Erythrocytes / enzymology
  • Female
  • Fibroblasts / enzymology
  • Glucosephosphate Dehydrogenase / analysis
  • Glucosephosphate Dehydrogenase / genetics
  • Granulocytes / enzymology
  • Heterozygote
  • Homozygote
  • Humans
  • Isoenzymes / analysis
  • Isoenzymes / genetics
  • Middle Aged
  • Thrombocytosis / enzymology
  • Thrombocytosis / genetics*

Substances

  • Isoenzymes
  • Glucosephosphate Dehydrogenase