Background: We review our experience with nine patients with partial unilateral lentiginosis (PUL), a rare pigmentary disorder.
Objective: Our purpose was to define the characteristics of PUL and to discuss the differential diagnosis.
Methods: The records of nine patients with PUL were reviewed. A literature review on diagnosis, association with other disorders, and differential diagnosis is presented.
Results: PUL is a rare benign disorder that has no known inheritance pattern and has no commonly associated abnormalities.
Conclusion: Careful history and physical examination may enable the distinction between PUL, nevus spilus, and other more serious genetic disorders associated with lentiginosis.