New mutations in the ataxia telangiectasia gene

Hum Genet. 1996 Aug;98(2):246-9. doi: 10.1007/s004390050202.

Abstract

We report the detection of four new mutations in the ataxia telangiectasia gene (ATM). Reverse-transcribed RNA extracted from cultured cells was analysed for mutations by polymerase chain reaction amplifications and restriction endonuclease fingerprinting. Three deletions and a base substitution are described. The deletions reported here would result in severe disruptions of the ATM gene product by leading either to a protein truncation (a 4-bp deletion) or the loss of stretches of 53 and 58 amino acids (a 159-bp deletion and a 174-bp deletion, respectively); whereas the base substitution would lead to an amino acid change from a highly conserved glycine to an arginine residue.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Amino Acid Sequence
  • Ataxia Telangiectasia / genetics*
  • Base Sequence
  • Cells, Cultured
  • Child
  • Child, Preschool
  • DNA Primers / genetics
  • DNA, Complementary / genetics
  • DNA, Complementary / isolation & purification
  • Female
  • Humans
  • Molecular Sequence Data
  • Mutation*
  • Point Mutation
  • RNA / genetics
  • Sequence Deletion
  • Sequence Homology, Amino Acid

Substances

  • DNA Primers
  • DNA, Complementary
  • RNA