KEGG   PATHWAY: cel00280
Entry
cel00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Caenorhabditis elegans (nematode)
Class
Metabolism; Amino acid metabolism
Pathway map
cel00280  Valine, leucine and isoleucine degradation
cel00280

Module
cel_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:cel00280]
cel_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:cel00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Caenorhabditis elegans (nematode) [GN:cel]
Gene
CELE_B0222.9  gad-3; putative aldehyde oxidase gad-3 [KO:K00157] [EC:1.2.3.1]
CELE_B0250.5  B0250.5; putative 3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K00020] [EC:1.1.1.31]
CELE_B0272.3  [KO:K00022] [EC:1.1.1.35]
CELE_B0303.3  hadb-1; putative 3-ketoacyl-CoA thiolase [KO:K07509] [EC:2.3.1.16]
CELE_C02B10.1  ivd-1; Isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
CELE_C05C10.3  C05C10.3; putative succinyl-CoA:3-ketoacid coenzyme A transferase, mitochondrial [KO:K01027] [EC:2.8.3.5]
CELE_C29F3.1  ech-1.1; Enoyl-CoA hydratase [KO:K07515] [EC:4.2.1.17 1.1.1.211]
CELE_C55B7.4  acdh-1; Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
CELE_D2030.5  mce-1; VOC domain-containing protein [KO:K05606] [EC:5.1.99.1]
CELE_F01F1.6  alh-9; Putative aldehyde dehydrogenase family 7 member A1 homolog [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
CELE_F01G10.2  ech-8; Enoyl-CoA Hydratase [KO:K00022] [EC:1.1.1.35]
CELE_F01G10.3  ech-9; Enoyl-CoA Hydratase [KO:K00022] [EC:1.1.1.35]
CELE_F01G4.2  ard-1; 3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
CELE_F02A9.10  mccc-2; putative methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
CELE_F09F7.4  hach-1; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial [KO:K05605] [EC:3.1.2.4]
CELE_F13D12.4  alh-8; putative methylmalonate-semialdehyde/malonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
CELE_F25B4.6  hmgs-1; Hydroxymethylglutaryl-CoA synthase [KO:K01641] [EC:2.3.3.10]
CELE_F27D4.5  bckd-1B; Transketolase-like pyrimidine-binding domain-containing protein [KO:K00167] [EC:1.2.4.4]
CELE_F27D9.5  pcca-1; Propionyl-CoA carboxylase alpha chain, mitochondrial [KO:K01965] [EC:6.4.1.3]
CELE_F28A10.6  acdh-9; Acyl CoA DeHydrogenase [KO:K11538] [EC:1.3.99.-]
CELE_F32B6.2  mccc-1; Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial [KO:K01968] [EC:6.4.1.4]
CELE_F42G9.5  alh-11; Aldehyde dehydrogenase domain-containing protein [KO:K00149] [EC:1.2.1.47 1.2.1.3]
CELE_F52E4.1  pccb-1; Propionyl-CoA carboxylase beta chain, mitochondrial [KO:K01966] [EC:6.4.1.3 2.1.3.15]
CELE_F53A2.7  acaa-2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
CELE_F54C8.1  F54C8.1; putative 3-hydroxyacyl-CoA dehydrogenase F54C8.1 [KO:K00022] [EC:1.1.1.35]
CELE_F54D8.3  alh-1; Aldehyde dehydrogenase domain-containing protein [KO:K00128] [EC:1.2.1.3]
CELE_F56B3.5  ech-5; Enoyl-CoA hydratase domain-containing protein 2, mitochondrial [KO:K05607] [EC:4.2.1.18]
CELE_K02A4.1  bcat-1; Branched-chain-amino-acid aminotransferase, cytosolic [KO:K00826] [EC:2.6.1.42]
CELE_K03A1.5  sur-5; Acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
CELE_K04D7.3  gta-1; putative 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
CELE_K04F1.15  alh-2; Aldehyde dehydrogenase domain-containing protein [KO:K00128] [EC:1.2.1.3]
CELE_K05F1.3  acdh-8; Medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
CELE_K06A5.6  acdh-3; Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
CELE_LLC1.3  dld-1; Dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
CELE_R09B5.6  hacd-1; Hydroxy-Acyl-CoA Dehydrogenase [KO:K00022] [EC:1.1.1.35]
CELE_T02G5.7  T02G5.7; Acetyl-CoA C-acetyltransferase [KO:K00626] [EC:2.3.1.9]
CELE_T02G5.8  kat-1; Acetyl-CoA acetyltransferase homolog, mitochondrial [KO:K00626] [EC:2.3.1.9]
CELE_T05G5.6  ech-6; putative enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
CELE_T05H4.13  alh-4; Aldehyde dehydrogenase [KO:K00128] [EC:1.2.1.3]
CELE_T08B1.3  alh-5; Aldehyde dehydrogenase [KO:K00128] [EC:1.2.1.3]
CELE_T08B2.7  ech-1.2; Enoyl-CoA hydratase [KO:K07515] [EC:4.2.1.17 1.1.1.211]
CELE_T08G2.3  acdh-10; putative medium-chain specific acyl-CoA dehydrogenase 10, mitochondrial [KO:K00249] [EC:1.3.8.7]
CELE_T09B4.8  T09B4.8; Alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
CELE_T10E9.9  acdh-4; Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
CELE_T25G12.5  acdh-7; Acyl-CoA dehydrogenase [KO:K00249] [EC:1.3.8.7]
CELE_Y105E8A.4  ech-7; Enoyl-CoA hydratase [KO:K07511] [EC:4.2.1.17]
CELE_Y39E4A.3  bckd-1A; 2-oxoisovalerate dehydrogenase subunit alpha [KO:K00166] [EC:1.2.4.4]
CELE_Y44A6D.5  Y44A6D.5; Branched-chain-amino-acid aminotransferase [KO:K00826] [EC:2.6.1.42]
CELE_Y69F12A.2  alh-12; Aldehyde dehydrogenase domain-containing protein [KO:K00149] [EC:1.2.1.47 1.2.1.3]
CELE_Y71G12B.10  Y71G12B.10; hydroxymethylglutaryl-CoA lyase [KO:K01640] [EC:4.1.3.4]
CELE_ZK1058.1  mmcm-1; putative methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
CELE_ZK669.4  dbt-1; Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
cel00020  Citrate cycle (TCA cycle)
cel00240  Pyrimidine metabolism
cel00290  Valine, leucine and isoleucine biosynthesis
cel00640  Propanoate metabolism
cel00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

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