U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Long segment coarctation of the aorta

MedGen UID:
1378073
Concept ID:
C4476935
Congenital Abnormality
HPO: HP:0031054

Definition

Coarctation of the aorta is a narrowing or constriction of a long segment of the arch of the aorta. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLong segment coarctation of the aorta

Professional guidelines

PubMed

Goubergrits L, Riesenkampff E, Yevtushenko P, Schaller J, Kertzscher U, Berger F, Kuehne T
Ann Biomed Eng 2015 Jan;43(1):168-76. Epub 2014 Sep 16 doi: 10.1007/s10439-014-1116-3. PMID: 25224077
Butera G, Heles M, Carminati M
Catheter Cardiovasc Interv 2011 Nov 15;78(6):933-9. Epub 2011 Aug 8 doi: 10.1002/ccd.23239. PMID: 21805575
Wang R, Sun LZ, Hu XP, Ma WG, Chang Q, Zhu JM, Liu YM, Yu CT
J Vasc Surg 2010 May;51(5):1203-8. Epub 2010 Mar 19 doi: 10.1016/j.jvs.2009.12.027. PMID: 20303693

Recent clinical studies

Etiology

Lamotte M, Paris C, Euvrard E, Pomero E, Schwartz C, Vené Y, Aubin F, Puzenat E
Arch Pediatr 2023 Aug;30(6):366-371. Epub 2023 May 13 doi: 10.1016/j.arcped.2023.03.009. PMID: 37188563
Choudhary P, Strugnell W, Puranik R, Hamilton-Craig C, Kutty S, Celermajer DS
Cardiol Young 2021 Sep;31(9):1445-1450. Epub 2021 Feb 26 doi: 10.1017/S104795112100038X. PMID: 33632344
Chen W, Fan C, Tang S, Zhou W, Iroegbu CD, Li J, Wu X, Yang J
Biomed Res Int 2020;2020:3805385. Epub 2020 May 14 doi: 10.1155/2020/3805385. PMID: 32509857Free PMC Article
Valeske K, Huber C, Mueller M, Böning A, Hijjeh N, Schranz D, Akintuerk H
Thorac Cardiovasc Surg 2011 Aug;59(5):293-7. Epub 2011 May 3 doi: 10.1055/s-0030-1271039. PMID: 21544788
Rao PS, Najjar HN, Mardini MK, Solymar L, Thapar MK
Am Heart J 1988 Mar;115(3):657-65. doi: 10.1016/0002-8703(88)90817-4. PMID: 2964188

Diagnosis

Lamotte M, Paris C, Euvrard E, Pomero E, Schwartz C, Vené Y, Aubin F, Puzenat E
Arch Pediatr 2023 Aug;30(6):366-371. Epub 2023 May 13 doi: 10.1016/j.arcped.2023.03.009. PMID: 37188563
Wang Y, Liu C, Zhang Y, Wang M
BMC Cardiovasc Disord 2021 Apr 13;21(1):176. doi: 10.1186/s12872-021-01987-7. PMID: 33849441Free PMC Article
Delmo Walter EM, Javier MFDM, Hetzer R
Interact Cardiovasc Thorac Surg 2017 Sep 1;25(3):400-406. doi: 10.1093/icvts/ivx115. PMID: 28498910
Valeske K, Huber C, Mueller M, Böning A, Hijjeh N, Schranz D, Akintuerk H
Thorac Cardiovasc Surg 2011 Aug;59(5):293-7. Epub 2011 May 3 doi: 10.1055/s-0030-1271039. PMID: 21544788
Rao PS
Semin Nephrol 1995 Mar;15(2):87-105. PMID: 7777727

Therapy

Chen W, Fan C, Tang S, Zhou W, Iroegbu CD, Li J, Wu X, Yang J
Biomed Res Int 2020;2020:3805385. Epub 2020 May 14 doi: 10.1155/2020/3805385. PMID: 32509857Free PMC Article
Sadiq M, Ur Rehman A, Qureshi AU, Qureshi SA
Catheter Cardiovasc Interv 2013 Oct 1;82(4):511-8. Epub 2013 Jun 18 doi: 10.1002/ccd.24945. PMID: 23592275
Valeske K, Huber C, Mueller M, Böning A, Hijjeh N, Schranz D, Akintuerk H
Thorac Cardiovasc Surg 2011 Aug;59(5):293-7. Epub 2011 May 3 doi: 10.1055/s-0030-1271039. PMID: 21544788
Celik T, Kursaklioglu H, Iyisoy A, Turhan H, Amasyali B, Kocaoglu M, Isik E
J Thorac Imaging 2006 Nov;21(4):296-9. doi: 10.1097/01.rti.0000213555.61752.3a. PMID: 17110855
Rao PS, Najjar HN, Mardini MK, Solymar L, Thapar MK
Am Heart J 1988 Mar;115(3):657-65. doi: 10.1016/0002-8703(88)90817-4. PMID: 2964188

Prognosis

Lamotte M, Paris C, Euvrard E, Pomero E, Schwartz C, Vené Y, Aubin F, Puzenat E
Arch Pediatr 2023 Aug;30(6):366-371. Epub 2023 May 13 doi: 10.1016/j.arcped.2023.03.009. PMID: 37188563
Wang Y, Liu C, Zhang Y, Wang M
BMC Cardiovasc Disord 2021 Apr 13;21(1):176. doi: 10.1186/s12872-021-01987-7. PMID: 33849441Free PMC Article
Nadorlik H, Bowman JL, Fitzgerald-Butt S, Mah ML, McBride KL, Kovalchin JP, Garg V
Pediatr Cardiol 2017 Dec;38(8):1709-1715. Epub 2017 Sep 25 doi: 10.1007/s00246-017-1740-4. PMID: 28948327Free PMC Article
Rao PS
Semin Nephrol 1995 Mar;15(2):87-105. PMID: 7777727
Rao PS, Najjar HN, Mardini MK, Solymar L, Thapar MK
Am Heart J 1988 Mar;115(3):657-65. doi: 10.1016/0002-8703(88)90817-4. PMID: 2964188

Clinical prediction guides

Lamotte M, Paris C, Euvrard E, Pomero E, Schwartz C, Vené Y, Aubin F, Puzenat E
Arch Pediatr 2023 Aug;30(6):366-371. Epub 2023 May 13 doi: 10.1016/j.arcped.2023.03.009. PMID: 37188563
Murakami AN, Croti UA, Cajueiro FCM, Arteaga G, Pike RB, Moscardini AC, Marchi CH, Cardoso MRR, Santos FCGB, Borim BC
Braz J Cardiovasc Surg 2021 Aug 6;36(4):461-467. doi: 10.21470/1678-9741-2020-0554. PMID: 34617427Free PMC Article
Wang Y, Liu C, Zhang Y, Wang M
BMC Cardiovasc Disord 2021 Apr 13;21(1):176. doi: 10.1186/s12872-021-01987-7. PMID: 33849441Free PMC Article
Chen W, Fan C, Tang S, Zhou W, Iroegbu CD, Li J, Wu X, Yang J
Biomed Res Int 2020;2020:3805385. Epub 2020 May 14 doi: 10.1155/2020/3805385. PMID: 32509857Free PMC Article
Nadorlik H, Bowman JL, Fitzgerald-Butt S, Mah ML, McBride KL, Kovalchin JP, Garg V
Pediatr Cardiol 2017 Dec;38(8):1709-1715. Epub 2017 Sep 25 doi: 10.1007/s00246-017-1740-4. PMID: 28948327Free PMC Article

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...