U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Autonomic status epilepticus

MedGen UID:
1719169
•Concept ID:
C5397685
•
Disease or Syndrome
HPO: HP:0032672

Definition

Autonomic status epilepticus is a type of non-convulsive status epilepticus without coma with prominent autonomic features regardless of whether it is electrographically generalized or focal. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAutonomic status epilepticus

Professional guidelines

PubMed

Critical Care Management of Anti-N-Methyl-D-Aspartate Receptor Encephalitis.
Neyens RR, Gaskill GE, Chalela JA
Crit Care Med 2018 Sep;46(9):1514-1521. doi: 10.1097/CCM.0000000000003268. PMID: 29927776
Autonomic seizures and autonomic status epilepticus peculiar to childhood: diagnosis and management.
Panayiotopoulos CP
Epilepsy Behav 2004 Jun;5(3):286-95. doi: 10.1016/j.yebeh.2004.01.013. PMID: 15145296

Recent clinical studies

Etiology

Panayiotopoulos Syndrome with a special emphasis of ictal semiologic features.
Yalçın AD, Ertaşoğlu Toydemir H
Epilepsy Res 2017 Mar;131:37-43. Epub 2017 Feb 16 doi: 10.1016/j.eplepsyres.2017.02.006. PMID: 28236737
Autonomic seizures and autonomic status epilepticus in early onset benign childhood occipital epilepsy (Panayiotopoulos syndrome).
Tedrus GM, Fonseca LC
Arq Neuropsiquiatr 2006 Sep;64(3B):723-6. doi: 10.1590/s0004-282x2006000500004. PMID: 17057874
Panayiotopoulos syndrome: a benign childhood autonomic epilepsy frequently imitating encephalitis, syncope, migraine, sleep disorder, or gastroenteritis.
Covanis A
Pediatrics 2006 Oct;118(4):e1237-43. Epub 2006 Sep 1 doi: 10.1542/peds.2006-0623. PMID: 16950946
Autonomic seizures and autonomic status epilepticus peculiar to childhood: diagnosis and management.
Panayiotopoulos CP
Epilepsy Behav 2004 Jun;5(3):286-95. doi: 10.1016/j.yebeh.2004.01.013. PMID: 15145296
Atypical evolution of Panayiotopoulos syndrome: a case report.
Ferrie CD, Koutroumanidis M, Rowlinson S, Sanders S, Panayiotopoulos CP
Epileptic Disord 2002 Mar;4(1):35-42. PMID: 11967178

Diagnosis

Benign childhood focal epilepsies: assessment of established and newly recognized syndromes.
Panayiotopoulos CP, Michael M, Sanders S, Valeta T, Koutroumanidis M
Brain 2008 Sep;131(Pt 9):2264-86. Epub 2008 Aug 21 doi: 10.1093/brain/awn162. PMID: 18718967
Autonomic status epilepticus in Panayiotopoulos syndrome and other childhood and adult epilepsies: a consensus view.
Ferrie CD, Caraballo R, Covanis A, Demirbilek V, Dervent A, Fejerman N, Fusco L, Grünewald RA, Kanazawa O, Koutroumanidis M, Lada C, Livingston JH, Nicotra A, Oguni H, Martinovic Z, Nordli DR Jr, Parisi P, Scott RC, Specchio N, Verrotti A, Vigevano F, Walker MC, Watanabe K, Yoshinaga H, Panayiotopoulos CP
Epilepsia 2007 Jun;48(6):1165-72. Epub 2007 Apr 18 doi: 10.1111/j.1528-1167.2007.01087.x. PMID: 17442005
Autonomic seizures and autonomic status epilepticus in early onset benign childhood occipital epilepsy (Panayiotopoulos syndrome).
Tedrus GM, Fonseca LC
Arq Neuropsiquiatr 2006 Sep;64(3B):723-6. doi: 10.1590/s0004-282x2006000500004. PMID: 17057874
Panayiotopoulos syndrome: a benign childhood autonomic epilepsy frequently imitating encephalitis, syncope, migraine, sleep disorder, or gastroenteritis.
Covanis A
Pediatrics 2006 Oct;118(4):e1237-43. Epub 2006 Sep 1 doi: 10.1542/peds.2006-0623. PMID: 16950946
Autonomic seizures and autonomic status epilepticus peculiar to childhood: diagnosis and management.
Panayiotopoulos CP
Epilepsy Behav 2004 Jun;5(3):286-95. doi: 10.1016/j.yebeh.2004.01.013. PMID: 15145296

Therapy

Efficacy and safety of levetiracetam in the treatment of Panayiotopoulos syndrome.
García C, Rubio G
Epilepsy Res 2009 Aug;85(2-3):318-20. Epub 2009 May 6 doi: 10.1016/j.eplepsyres.2009.03.024. PMID: 19423296
Panayiotopoulos syndrome: a benign childhood autonomic epilepsy frequently imitating encephalitis, syncope, migraine, sleep disorder, or gastroenteritis.
Covanis A
Pediatrics 2006 Oct;118(4):e1237-43. Epub 2006 Sep 1 doi: 10.1542/peds.2006-0623. PMID: 16950946
Children with Rolandic spikes and ictal vomiting: Rolandic epilepsy or Panayiotopoulos syndrome?
Covanis A, Lada C, Skiadas K
Epileptic Disord 2003 Sep;5(3):139-43. PMID: 14684348

Prognosis

Panayiotopoulos Syndrome with a special emphasis of ictal semiologic features.
Yalçın AD, Ertaşoğlu Toydemir H
Epilepsy Res 2017 Mar;131:37-43. Epub 2017 Feb 16 doi: 10.1016/j.eplepsyres.2017.02.006. PMID: 28236737
Benign childhood focal epilepsies: assessment of established and newly recognized syndromes.
Panayiotopoulos CP, Michael M, Sanders S, Valeta T, Koutroumanidis M
Brain 2008 Sep;131(Pt 9):2264-86. Epub 2008 Aug 21 doi: 10.1093/brain/awn162. PMID: 18718967
Panayiotopoulos syndrome: a benign childhood autonomic epilepsy frequently imitating encephalitis, syncope, migraine, sleep disorder, or gastroenteritis.
Covanis A
Pediatrics 2006 Oct;118(4):e1237-43. Epub 2006 Sep 1 doi: 10.1542/peds.2006-0623. PMID: 16950946
Autonomic seizures and autonomic status epilepticus peculiar to childhood: diagnosis and management.
Panayiotopoulos CP
Epilepsy Behav 2004 Jun;5(3):286-95. doi: 10.1016/j.yebeh.2004.01.013. PMID: 15145296
A study of 43 patients with panayiotopoulos syndrome, a common and benign childhood seizure susceptibility.
Lada C, Skiadas K, Theodorou V, Loli N, Covanis A
Epilepsia 2003 Jan;44(1):81-8. doi: 10.1046/j.1528-1157.2003.32602.x. PMID: 12581234

Clinical prediction guides

Panayiotopoulos Syndrome with a special emphasis of ictal semiologic features.
Yalçın AD, Ertaşoğlu Toydemir H
Epilepsy Res 2017 Mar;131:37-43. Epub 2017 Feb 16 doi: 10.1016/j.eplepsyres.2017.02.006. PMID: 28236737
Benign childhood focal epilepsies: assessment of established and newly recognized syndromes.
Panayiotopoulos CP, Michael M, Sanders S, Valeta T, Koutroumanidis M
Brain 2008 Sep;131(Pt 9):2264-86. Epub 2008 Aug 21 doi: 10.1093/brain/awn162. PMID: 18718967
Autonomic seizures and autonomic status epilepticus in early onset benign childhood occipital epilepsy (Panayiotopoulos syndrome).
Tedrus GM, Fonseca LC
Arq Neuropsiquiatr 2006 Sep;64(3B):723-6. doi: 10.1590/s0004-282x2006000500004. PMID: 17057874

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...