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Maxillofacial Desmoplastic Fibroma

MedGen UID:
1764248
•Concept ID:
C5420441
•
Neoplastic Process

Definition

A rare, benign, locally aggressive osteolytic neoplasm that arises in a maxillofacial bone. It is characterized by the presence of a rich collagenous stroma and spindle cells with minimal cellular atypia. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMaxillofacial Desmoplastic Fibroma

Professional guidelines

PubMed

Management of fibro-osseous lesions of the craniofacial area. Presentation of 19 cases and review of the literature.
Suarez-Soto A, Baquero-Ruiz de la Hermosa MC, Minguez-Martínez I, Floría-García LM, Barea-Gámiz J, Delhom-Valero J, Risueño-Mata P
Med Oral Patol Oral Cir Bucal 2013 May 1;18(3):e479-85. doi: 10.4317/medoral.18289. PMID: 23524411Free PMC Article

Recent clinical studies

Etiology

Myofibroblastoma of the mandible in a 3-year-old child.
Hajeri S, Al Jabab A, Al Sheddi M, Fatani H
Oral Maxillofac Surg 2016 Mar;20(1):103-7. Epub 2015 Aug 19 doi: 10.1007/s10006-015-0524-3. PMID: 26282517
Desmoplastic fibroma of the mandible: report of a misdiagnosed case.
Guerrero JS, Ruiz CA, Al-Jandan BA, Bustillo JA
J Mich Dent Assoc 2014 Mar;96(3):30-3. PMID: 24961082
Management of fibro-osseous lesions of the craniofacial area. Presentation of 19 cases and review of the literature.
Suarez-Soto A, Baquero-Ruiz de la Hermosa MC, Minguez-Martínez I, Floría-García LM, Barea-Gámiz J, Delhom-Valero J, Risueño-Mata P
Med Oral Patol Oral Cir Bucal 2013 May 1;18(3):e479-85. doi: 10.4317/medoral.18289. PMID: 23524411Free PMC Article
Desmoplastic fibroma of the mandible in a child: report of a case.
Templeton K, Glass N, Young SK
Oral Surg Oral Med Oral Pathol Oral Radiol Endod 1997 Dec;84(6):620-3. doi: 10.1016/s1079-2104(97)90362-0. PMID: 9431529
Fibromatoses of the oral and paraoral soft tissues and jaws. Review of the literature and report of 12 new cases.
Vally IM, Altini M
Oral Surg Oral Med Oral Pathol 1990 Feb;69(2):191-8. doi: 10.1016/0030-4220(90)90327-o. PMID: 2406675

Diagnosis

Pediatric Gnathic Bony and Mesenchymal Tumors.
Liu Y, Housley Smith M, Patel PB, Bilodeau EA
Pediatr Dev Pathol 2023 Nov-Dec;26(6):621-641. Epub 2023 May 26 doi: 10.1177/10935266231170744. PMID: 37232383
Desmoplastic fibroma associated with tuberous sclerosis: case report and literature review.
Fahmy MD, Gupta A, Padilla RJ, Segura A, Brookes CD
Oral Surg Oral Med Oral Pathol Oral Radiol 2019 Aug;128(2):e92-e99. Epub 2019 Mar 16 doi: 10.1016/j.oooo.2019.03.008. PMID: 31078508
Desmoplastic fibroma of the mandible: report of a misdiagnosed case.
Guerrero JS, Ruiz CA, Al-Jandan BA, Bustillo JA
J Mich Dent Assoc 2014 Mar;96(3):30-3. PMID: 24961082
Management of fibro-osseous lesions of the craniofacial area. Presentation of 19 cases and review of the literature.
Suarez-Soto A, Baquero-Ruiz de la Hermosa MC, Minguez-Martínez I, Floría-García LM, Barea-Gámiz J, Delhom-Valero J, Risueño-Mata P
Med Oral Patol Oral Cir Bucal 2013 May 1;18(3):e479-85. doi: 10.4317/medoral.18289. PMID: 23524411Free PMC Article
Odontogenic fibroma.
Dunlap CL
Semin Diagn Pathol 1999 Nov;16(4):293-6. PMID: 10587271

Prognosis

Bilateral collagenous fibroma of the hard palate: a case report and review of the literature.
El-Naggar HA, El-Mahallawy YA, Harby MI, Abou Madawi NA
J Med Case Rep 2023 Jan 7;17(1):5. doi: 10.1186/s13256-022-03691-2. PMID: 36609451Free PMC Article
Desmoplastic fibroma of the mandible: a series of three cases and review of literature.
Woods TR, Cohen DM, Islam MN, Rawal Y, Bhattacharyya I
Head Neck Pathol 2015 Jun;9(2):196-204. Epub 2014 Aug 12 doi: 10.1007/s12105-014-0561-5. PMID: 25113037Free PMC Article
Desmoplastic fibroma of the mandible: report of a misdiagnosed case.
Guerrero JS, Ruiz CA, Al-Jandan BA, Bustillo JA
J Mich Dent Assoc 2014 Mar;96(3):30-3. PMID: 24961082
Desmoplastic fibroma of the mandible--review of the literature and presentation of a rare case.
Schneider M, Zimmermann AC, Depprich RA, Kübler NR, Engers R, Naujoks CD, Handschel J
Head Face Med 2009 Nov 24;5:25. doi: 10.1186/1746-160X-5-25. PMID: 19930688Free PMC Article
Odontogenic fibroma.
Dunlap CL
Semin Diagn Pathol 1999 Nov;16(4):293-6. PMID: 10587271

Clinical prediction guides

Unraveling the challenges in the diagnosis and management of desmoplastic fibroma of the mandible-a case report.
Siddiqui HK, Khan SA, Aijaz A, Qureshi MB
BMC Oral Health 2024 Feb 20;24(1):256. doi: 10.1186/s12903-024-04018-x. PMID: 38378640Free PMC Article

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