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Necrotizing pulmonary granulomatosis

MedGen UID:
1785597
Concept ID:
C5539676
Disease or Syndrome
Synonym: Caseating pulmonary granulomatosis
 
HPO: HP:0033550

Definition

A granuloma that is associated with necrotic changes. Caseation necrosis is defined as a region in granulomas with eosinophilic, granular and cheese-like cellular debris with necrosis. The word caseous itself means pertaining or related to cheese, and comes from the Latin word caseus, meaning cheese. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNecrotizing pulmonary granulomatosis

Professional guidelines

PubMed

Anaev EK, Baranova IA, Belevsky AS
Ter Arkh 2018 Apr 19;90(3):99-106. doi: 10.26442/terarkh201890399-106. PMID: 30701864
Comarmond C, Cacoub P
Autoimmun Rev 2014 Nov;13(11):1121-5. Epub 2014 Aug 20 doi: 10.1016/j.autrev.2014.08.017. PMID: 25149391
Ozen S, Pistorio A, Iusan SM, Bakkaloglu A, Herlin T, Brik R, Buoncompagni A, Lazar C, Bilge I, Uziel Y, Rigante D, Cantarini L, Hilario MO, Silva CA, Alegria M, Norambuena X, Belot A, Berkun Y, Estrella AI, Olivieri AN, Alpigiani MG, Rumba I, Sztajnbok F, Tambic-Bukovac L, Breda L, Al-Mayouf S, Mihaylova D, Chasnyk V, Sengler C, Klein-Gitelman M, Djeddi D, Nuno L, Pruunsild C, Brunner J, Kondi A, Pagava K, Pederzoli S, Martini A, Ruperto N; Paediatric Rheumatology International Trials Organisation (PRINTO)
Ann Rheum Dis 2010 May;69(5):798-806. doi: 10.1136/ard.2009.116657. PMID: 20413568

Recent clinical studies

Etiology

Chevet B, Cornec D, Casal Moura M, Cornec-Le Gall E, Fervenza FC, Warrington KJ, Specks U, Berti A
Rheumatology (Oxford) 2023 May 2;62(5):1787-1803. doi: 10.1093/rheumatology/keac623. PMID: 36315063
Honsová E
Cesk Patol 2020 Spring;56(2):68-73. PMID: 32493022
Anaev EK, Baranova IA, Belevsky AS
Ter Arkh 2018 Apr 19;90(3):99-106. doi: 10.26442/terarkh201890399-106. PMID: 30701864
Ozen S, Pistorio A, Iusan SM, Bakkaloglu A, Herlin T, Brik R, Buoncompagni A, Lazar C, Bilge I, Uziel Y, Rigante D, Cantarini L, Hilario MO, Silva CA, Alegria M, Norambuena X, Belot A, Berkun Y, Estrella AI, Olivieri AN, Alpigiani MG, Rumba I, Sztajnbok F, Tambic-Bukovac L, Breda L, Al-Mayouf S, Mihaylova D, Chasnyk V, Sengler C, Klein-Gitelman M, Djeddi D, Nuno L, Pruunsild C, Brunner J, Kondi A, Pagava K, Pederzoli S, Martini A, Ruperto N; Paediatric Rheumatology International Trials Organisation (PRINTO)
Ann Rheum Dis 2010 May;69(5):798-806. doi: 10.1136/ard.2009.116657. PMID: 20413568
Lane SE, Watts R, Scott DG
Curr Rheumatol Rep 2005 Aug;7(4):270-5. doi: 10.1007/s11926-005-0036-5. PMID: 16045829

Diagnosis

Chevet B, Cornec D, Casal Moura M, Cornec-Le Gall E, Fervenza FC, Warrington KJ, Specks U, Berti A
Rheumatology (Oxford) 2023 May 2;62(5):1787-1803. doi: 10.1093/rheumatology/keac623. PMID: 36315063
Rosen Y
Arch Pathol Lab Med 2022 Jan 2;146(2):233-251. doi: 10.5858/arpa.2020-0543-RA. PMID: 33905479
Sève P, Pacheco Y, Durupt F, Jamilloux Y, Gerfaud-Valentin M, Isaac S, Boussel L, Calender A, Androdias G, Valeyre D, El Jammal T
Cells 2021 Mar 31;10(4) doi: 10.3390/cells10040766. PMID: 33807303Free PMC Article
Sacoto G, Boukhlal S, Specks U, Flores-Suárez LF, Cornec D
Presse Med 2020 Oct;49(3):104039. Epub 2020 Jul 7 doi: 10.1016/j.lpm.2020.104039. PMID: 32650042
Gafoor K, Patel S, Girvin F, Gupta N, Naidich D, Machnicki S, Brown KK, Mehta A, Husta B, Ryu JH, Sarosi GA, Franquet T, Verschakelen J, Johkoh T, Travis W, Raoof S
Chest 2018 Jun;153(6):1443-1465. Epub 2018 Mar 6 doi: 10.1016/j.chest.2018.02.026. PMID: 29518379

Therapy

Falde SD, Fussner LA, Tazelaar HD, O'Brien EK, Lamprecht P, Konig MF, Specks U
Lancet Rheumatol 2024 May;6(5):e314-e327. Epub 2024 Apr 1 doi: 10.1016/S2665-9913(24)00035-3. PMID: 38574742
Chevet B, Cornec D, Casal Moura M, Cornec-Le Gall E, Fervenza FC, Warrington KJ, Specks U, Berti A
Rheumatology (Oxford) 2023 May 2;62(5):1787-1803. doi: 10.1093/rheumatology/keac623. PMID: 36315063
Puéchal X
Joint Bone Spine 2020 Dec;87(6):572-578. Epub 2020 Jun 17 doi: 10.1016/j.jbspin.2020.06.005. PMID: 32562697
Comarmond C, Cacoub P
Autoimmun Rev 2014 Nov;13(11):1121-5. Epub 2014 Aug 20 doi: 10.1016/j.autrev.2014.08.017. PMID: 25149391
Leavitt RY, Fauci AS
Am Rev Respir Dis 1986 Jul;134(1):149-66. doi: 10.1164/arrd.1986.134.1.149. PMID: 2873770

Prognosis

Chevet B, Cornec D, Casal Moura M, Cornec-Le Gall E, Fervenza FC, Warrington KJ, Specks U, Berti A
Rheumatology (Oxford) 2023 May 2;62(5):1787-1803. doi: 10.1093/rheumatology/keac623. PMID: 36315063
Puéchal X
Joint Bone Spine 2020 Dec;87(6):572-578. Epub 2020 Jun 17 doi: 10.1016/j.jbspin.2020.06.005. PMID: 32562697
Comarmond C, Cacoub P
Autoimmun Rev 2014 Nov;13(11):1121-5. Epub 2014 Aug 20 doi: 10.1016/j.autrev.2014.08.017. PMID: 25149391
Lynch JP 3rd, Kazerooni EA, Gay SE
Clin Chest Med 1997 Dec;18(4):755-85. doi: 10.1016/s0272-5231(05)70417-2. PMID: 9413657
Leavitt RY, Fauci AS
Am Rev Respir Dis 1986 Jul;134(1):149-66. doi: 10.1164/arrd.1986.134.1.149. PMID: 2873770

Clinical prediction guides

Bataille PM, Durel CA, Chauveau D, Panes A, Thervet ÉS, Terrier B
J Autoimmun 2022 Dec;133:102910. Epub 2022 Sep 12 doi: 10.1016/j.jaut.2022.102910. PMID: 36108505
Yang M, Rosenthal AC, Ashman JB, Craig FE
Curr Probl Diagn Radiol 2021 May-Jun;50(3):443-449. Epub 2019 Feb 10 doi: 10.1067/j.cpradiol.2019.02.002. PMID: 30826140
Alba MA, Jennette JC, Falk RJ
Semin Respir Crit Care Med 2018 Aug;39(4):413-424. Epub 2018 Nov 7 doi: 10.1055/s-0038-1673386. PMID: 30404109Free PMC Article
Comarmond C, Cacoub P
Autoimmun Rev 2014 Nov;13(11):1121-5. Epub 2014 Aug 20 doi: 10.1016/j.autrev.2014.08.017. PMID: 25149391
Guillevin L
Rheumatology (Oxford) 2009 Jun;48 Suppl 3:iii54-7. doi: 10.1093/rheumatology/ken484. PMID: 19487226

Recent systematic reviews

Hajishah H, Amini MJ, Chadeganipour AS, Salehi SA, Kazemi D
Curr Rheumatol Rev 2024;20(3):270-283. doi: 10.2174/0115733971263964231020072640. PMID: 37907486

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