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Secondary polyarteritis nodosa

MedGen UID:: 1843373
•Concept ID:: C5680050
•: Disease or Syndrome

Synonyms:	Scondary PAN; secondary PAN; Secondary PAN; Secondary periarteritis nodosa; secondary periarteritis nodosa; secondary polyarteritis nodosa
Modes of inheritance:	Not genetically inherited MedGen UID: 988794 •Concept ID: CN307044 • Finding Source: Orphanet clinical entity without genetic inheritance. See: This record Not genetically inherited (Orphanet)

Monarch Initiative:	MONDO:0018594
Orphanet:	ORPHA439746

Definition

Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN (see this term) characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV). [from ORDO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVSecondary polyarteritis nodosa

Abnormal cardiovascular system morphology
- Abnormal vascular morphology
  - Abnormal blood vessel morphology
    - Abnormal systemic arterial morphology
      - Arteritis
        Polyarteritis nodosa
        Secondary polyarteritis nodosa

Professional guidelines

PubMed

Atypical wounds. Best clinical practice and challenges.

Isoherranen K, O'Brien JJ, Barker J, Dissemond J, Hafner J, Jemec GBE, Kamarachev J, Läuchli S, Montero EC, Nobbe S, Sunderkötter C, Velasco ML
J Wound Care 2019 Jun 1;28(Sup6):S1-S92. doi: 10.12968/jowc.2019.28.Sup6.S1. PMID: 31169055

Classification and classification criteria for vasculitis: achievements, limitations and prospects.

Mahr A, de Menthon M
Curr Opin Rheumatol 2015 Jan;27(1):1-9. doi: 10.1097/BOR.0000000000000134. PMID: 25415531

Recent understanding on diagnosis and management of central nervous system vasculitis in children.

Iannetti L, Zito R, Bruschi S, Papetti L, Ulgiati F, Nicita F, Del Balzo F, Spalice A
Clin Dev Immunol 2012;2012:698327. Epub 2012 Sep 12 doi: 10.1155/2012/698327. PMID: 23008735 Free PMC Article

See all (9)

Recent clinical studies

Etiology

Imaging in small and medium vessel vasculitis.

Singhal M, Gupta P, Sharma A
Int J Rheum Dis 2019 Jan;22 Suppl 1:78-85. doi: 10.1111/1756-185X.13390. PMID: 30698353

What's new in autoinflammation?

Ozen S
Pediatr Nephrol 2019 Dec;34(12):2449-2456. Epub 2018 Dec 14 doi: 10.1007/s00467-018-4155-4. PMID: 30552566

Cardiac disease in familial Mediterranean fever.

Erken E, Erken E
Rheumatol Int 2018 Jan;38(1):51-58. Epub 2017 Oct 20 doi: 10.1007/s00296-017-3853-8. PMID: 29051974

CNS vasculitis.

Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421

Vasculitis.

Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

See all (56)

Diagnosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.

Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399

What's new in autoinflammation?

Ozen S
Pediatr Nephrol 2019 Dec;34(12):2449-2456. Epub 2018 Dec 14 doi: 10.1007/s00467-018-4155-4. PMID: 30552566

Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.

Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365

Headache and vasculitis.

Lopez JI, Holdridge A, Chalela J
Curr Pain Headache Rep 2013 Mar;17(3):320. doi: 10.1007/s11916-012-0320-9. PMID: 23338772

Vasculitis.

Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

See all (121)

Therapy

Efficacy and safety of treatments in cutaneous polyarteritis nodosa: A French observational retrospective study.

Bettuzzi T, Jachiet M, Sbidian E, Frumholtz L, Cordoliani F, Mouthon L, Chasset F, Paule R, Bouaziz JD, Guillevin L, Terrier B, Aractingi S, Dupin N, Régent A
J Am Acad Dermatol 2022 May;86(5):1035-1041. Epub 2021 Jul 2 doi: 10.1016/j.jaad.2021.06.872. PMID: 34224771

Cardiac disease in familial Mediterranean fever.

Erken E, Erken E
Rheumatol Int 2018 Jan;38(1):51-58. Epub 2017 Oct 20 doi: 10.1007/s00296-017-3853-8. PMID: 29051974

Systemic vasculitis and the gut.

Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357

Vasculitic neuropathies.

Burns TM, Schaublin GA, Dyck PJ
Neurol Clin 2007 Feb;25(1):89-113. doi: 10.1016/j.ncl.2006.11.002. PMID: 17324722

Primary and secondary vasculitic neuropathy.

Said G, Lacroix C
J Neurol 2005 Jun;252(6):633-41. Epub 2005 Apr 5 doi: 10.1007/s00415-005-0833-9. PMID: 15806339

See all (59)

Prognosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.

Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399

Polyarteritis Nodosa: State of the art.

Puéchal X
Joint Bone Spine 2022 Jul;89(4):105320. Epub 2021 Dec 11 doi: 10.1016/j.jbspin.2021.105320. PMID: 34902576

Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.

Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365

CNS vasculitis.

Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421

Polyarteritis nodosa.

Bonsib SM
Semin Diagn Pathol 2001 Feb;18(1):14-23. PMID: 11296989

See all (55)

Clinical prediction guides

Clinical features and long-term outcomes of patients with systemic polyarteritis nodosa diagnosed since 2005: Data from 196 patients.

Rohmer J, Nguyen Y, Trefond L, Agard C, Allain JS, Berezne A, Charles P, Cohen P, Gondran G, Groh M, Huscenot T, Lacout C, Lazaro E, London J, Maurier F, Mekinian A, Mesbah R, Nubourgh I, Perard L, Puéchal X, Pugnet G, Puyade M, Queyrel V, Roux A, Rouzaud D, Durel CA, Guillevin L, Terrier B; French Vasculitis Study Group (FVSG)
J Autoimmun 2023 Sep;139:103093. Epub 2023 Aug 1 doi: 10.1016/j.jaut.2023.103093. PMID: 37536165

Efficacy and safety of treatments in cutaneous polyarteritis nodosa: A French observational retrospective study.

Imaging in small and medium vessel vasculitis.

Singhal M, Gupta P, Sharma A
Int J Rheum Dis 2019 Jan;22 Suppl 1:78-85. doi: 10.1111/1756-185X.13390. PMID: 30698353

Systemic vasculitis and the gut.

Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357

Vasculitis.

Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

See all (25)

Recent systematic reviews

Inflammatory muscle involvement in systemic vasculitis: A systematic review.

Conticini E, d'Alessandro M, Al Khayyat SG, D'Alessandro R, D'Ignazio E, Pata AP, Vallifuoco G, Falsetti P, Baldi C, Bardelli M, Gentileschi S, Fabiani C, Mazzei MA, Guarnieri A, Bargagli E, Cantarini L, Frediani B
Autoimmun Rev 2022 Mar;21(3):103029. Epub 2021 Dec 29 doi: 10.1016/j.autrev.2021.103029. PMID: 34971804

Dermatological Manifestations in Pediatric Inflammatory Bowel Disease.

Diaconescu S, Strat S, Balan GG, Anton C, Stefanescu G, Ioniuc I, Stanescu AMA
Medicina (Kaunas) 2020 Aug 23;56(9) doi: 10.3390/medicina56090425. PMID: 32842528 Free PMC Article

Haemophagocytic syndrome in rheumatic patients. A systematic review.

Atteritano M, David A, Bagnato G, Beninati C, Frisina A, Iaria C, Bagnato G, Cascio A
Eur Rev Med Pharmacol Sci 2012 Oct;16(10):1414-24. PMID: 23104659

See all (3)

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Secondary polyarteritis nodosa

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Therapy

Prognosis

Clinical prediction guides

Recent systematic reviews

Supplemental Content

Table of contents

Clinical resources

Practice guidelines

Consumer resources

Reviews

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