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Chest Wall Plexiform Fibrohistiocytic Tumor

MedGen UID:
272455
•Concept ID:
C1332935
•
Neoplastic Process
Synonyms: Chest Wall Plexiform Fibrohistiocytic Neoplasm; Plexiform Fibrohistiocytic Neoplasm of Chest Wall; Plexiform Fibrohistiocytic Neoplasm of the Chest Wall; Plexiform Fibrohistiocytic Tumor of Chest Wall; Plexiform Fibrohistiocytic Tumor of the Chest Wall

Definition

An intermediate fibrohistiocytic neoplasm arising from the skin in the chest wall. It is a multinodular poorly circumscribed tumor, characterized by the presence of multinucleated giant cells, mononuclear histiocyte-like cells, and spindle fibroblast-like cells arranged in a plexiform pattern. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChest Wall Plexiform Fibrohistiocytic Tumor

Recent clinical studies

Etiology

Plexiform Myofibroblastoma: Clinicopathologic Analysis of 36 Cases of a Distinctive Benign Tumor of Soft Tissue Affecting Mainly Children and Young Adults.
Papke DJ Jr, Al-Ibraheemi A, Fletcher CDM
Am J Surg Pathol 2020 Nov;44(11):1469-1478. doi: 10.1097/PAS.0000000000001534. PMID: 32618598

Diagnosis

Plexiform fibrohistiocytic tumor on the chest of a 5-year-old child and review of the literature.
Valiga A, Neidig L, Cusack CA, Gaddis K, Jen M, Rubin A, Moon AT
Pediatr Dermatol 2019 Jul;36(4):490-496. Epub 2019 Mar 11 doi: 10.1111/pde.13805. PMID: 30859648
Fine needle aspiration cytology of plexiform fibrohistiocytic tumor. A case report.
Redlich G, Bocklage T, Joste N
Acta Cytol 1999 Sep-Oct;43(5):867-72. doi: 10.1159/000331306. PMID: 10518146

Prognosis

Plexiform fibrohistiocytic tumor on the chest of a 5-year-old child and review of the literature.
Valiga A, Neidig L, Cusack CA, Gaddis K, Jen M, Rubin A, Moon AT
Pediatr Dermatol 2019 Jul;36(4):490-496. Epub 2019 Mar 11 doi: 10.1111/pde.13805. PMID: 30859648

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