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Ocular adnexal lymphoma

MedGen UID:
453939
Concept ID:
C2981712
Neoplastic Process
Synonyms: non-Hodgkin lymphoma of ocular adnexa; OAL; ocular adnexa non-Hodgkin lymphoma; Ocular Adnexal Lymphoma; ocular adnexal lymphoma; Ocular Adnexal Non-Hodgkin Lymphoma; Primary Ocular Adnexal Lymphoma; Primary Ocular Adnexal Non-Hodgkin Lymphoma
 
Monarch Initiative: MONDO:0020646

Definition

A non-Hodgkin lymphoma arising from the conjunctiva, lacrimal gland, lacrimal drainage apparatus, eyelids, or other orbital tissues around the eye. The vast majority of cases are extranodal marginal zone lymphomas of mucosa-associated lymphoid tissue, however, other histologic types of lymphomas can originate from ocular adnexal tissues, including rare cases of NK/T-cell lymphomas of nasal type. [from NCI]

Professional guidelines

PubMed

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Aronow ME
Int Ophthalmol Clin 2015 Winter;55(1):97-109. doi: 10.1097/IIO.0000000000000049. PMID: 25436496
Ferreri AJ, Assanelli A, Crocchiolo R, Dognini GP, Resti AG, Politi LS, Doglioni C, Cappio FC, Dolcetti R, Ponzoni M
Expert Opin Pharmacother 2007 Jun;8(8):1073-83. doi: 10.1517/14656566.8.8.1073. PMID: 17922636

Recent clinical studies

Etiology

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Castillejo Becerra CM, Dalvin LA, Jevremovic D, Hodge DO, Tooley AA
Orbit 2022 Feb;41(1):97-104. Epub 2022 Jan 4 doi: 10.1080/01676830.2021.2018715. PMID: 35100932
Hsu CR, Chen YY, Yao M, Wei YH, Hsieh YT, Liao SL
Eye (Lond) 2021 Jul;35(7):1946-1953. Epub 2020 Sep 29 doi: 10.1038/s41433-020-01198-y. PMID: 32994547Free PMC Article
Mulay K, Honavar SG
Semin Diagn Pathol 2016 May;33(3):164-72. Epub 2015 Oct 23 doi: 10.1053/j.semdp.2015.10.004. PMID: 26972223
Özkan MC, Palamar M, Tombuloğlu M, Hekimgil M, Özsan N, Saydam G, Şahin F
Clin Lymphoma Myeloma Leuk 2015 Jun;15 Suppl:S158-60. doi: 10.1016/j.clml.2015.02.015. PMID: 26297270

Diagnosis

Kirkegaard MK
Acta Ophthalmol 2022 Oct;100 Suppl 270:3-37. doi: 10.1111/aos.15248. PMID: 36196757
Loya A, Ramachandran V, Ayaz T, Weng CY
BMC Ophthalmol 2021 Apr 7;21(1):162. doi: 10.1186/s12886-021-01921-7. PMID: 33827494Free PMC Article
Maheshwari A, Finger PT
Cancer Metastasis Rev 2018 Dec;37(4):677-690. doi: 10.1007/s10555-018-9762-9. PMID: 30203109
Svendsen FH, Heegaard S
Surv Ophthalmol 2017 May-Jun;62(3):312-331. Epub 2016 Nov 26 doi: 10.1016/j.survophthal.2016.11.009. PMID: 27894880
Mulay K, Honavar SG
Semin Diagn Pathol 2016 May;33(3):164-72. Epub 2015 Oct 23 doi: 10.1053/j.semdp.2015.10.004. PMID: 26972223

Therapy

Aronow ME
Int Ophthalmol Clin 2015 Winter;55(1):97-109. doi: 10.1097/IIO.0000000000000049. PMID: 25436496
Prat MC, Surapaneni K, Chalian H, DeLaPaz RL, Kazim M
Ophthalmic Plast Reconstr Surg 2013 Nov-Dec;29(6):424-7. doi: 10.1097/IOP.0b013e3182916495. PMID: 24220098
Shome D, Esmaeli B
Curr Opin Ophthalmol 2008 Sep;19(5):414-21. doi: 10.1097/ICU.0b013e32830b1539. PMID: 18772675
Ferreri AJ, Dolcetti R, Du MQ, Doglioni C, Resti AG, Politi LS, De Conciliis C, Radford J, Bertoni F, Zucca E, Cavalli F, Ponzoni M
Ann Oncol 2008 May;19(5):835-46. Epub 2007 Nov 6 doi: 10.1093/annonc/mdm513. PMID: 17986622
Ferreri AJ, Assanelli A, Crocchiolo R, Dognini GP, Resti AG, Politi LS, Doglioni C, Cappio FC, Dolcetti R, Ponzoni M
Expert Opin Pharmacother 2007 Jun;8(8):1073-83. doi: 10.1517/14656566.8.8.1073. PMID: 17922636

Prognosis

Kirkegaard MK
Acta Ophthalmol 2022 Oct;100 Suppl 270:3-37. doi: 10.1111/aos.15248. PMID: 36196757
Hsu CR, Chen YY, Yao M, Wei YH, Hsieh YT, Liao SL
Eye (Lond) 2021 Jul;35(7):1946-1953. Epub 2020 Sep 29 doi: 10.1038/s41433-020-01198-y. PMID: 32994547Free PMC Article
Svendsen FH, Heegaard S
Surv Ophthalmol 2017 May-Jun;62(3):312-331. Epub 2016 Nov 26 doi: 10.1016/j.survophthal.2016.11.009. PMID: 27894880
Mulay K, Honavar SG
Semin Diagn Pathol 2016 May;33(3):164-72. Epub 2015 Oct 23 doi: 10.1053/j.semdp.2015.10.004. PMID: 26972223
Özkan MC, Palamar M, Tombuloğlu M, Hekimgil M, Özsan N, Saydam G, Şahin F
Clin Lymphoma Myeloma Leuk 2015 Jun;15 Suppl:S158-60. doi: 10.1016/j.clml.2015.02.015. PMID: 26297270

Clinical prediction guides

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Kirkegaard MK
Acta Ophthalmol 2022 Oct;100 Suppl 270:3-37. doi: 10.1111/aos.15248. PMID: 36196757
Maheshwari A, Finger PT
Cancer Metastasis Rev 2018 Dec;37(4):677-690. doi: 10.1007/s10555-018-9762-9. PMID: 30203109
Ferreri AJ, Dolcetti R, Du MQ, Doglioni C, Resti AG, Politi LS, De Conciliis C, Radford J, Bertoni F, Zucca E, Cavalli F, Ponzoni M
Ann Oncol 2008 May;19(5):835-46. Epub 2007 Nov 6 doi: 10.1093/annonc/mdm513. PMID: 17986622
Ferreri AJ, Assanelli A, Crocchiolo R, Dognini GP, Resti AG, Politi LS, Doglioni C, Cappio FC, Dolcetti R, Ponzoni M
Expert Opin Pharmacother 2007 Jun;8(8):1073-83. doi: 10.1517/14656566.8.8.1073. PMID: 17922636

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