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Extrahepatic Bile Duct Neuroendocrine Neoplasm

MedGen UID:
474771
Concept ID:
C3273138
Neoplastic Process

Definition

A neoplasm with neuroendocrine differentiation that arises from the extrahepatic bile ducts. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). [from NCI]

Professional guidelines

PubMed

Komiyama S, Okusaka T, Maruki Y, Ohba A, Nagashio Y, Kondo S, Hijioka S, Morizane C, Ueno H, Sukeda A, Mizui T, Takamoto T, Nara S, Ban D, Esaki M, Hiraoka N, Shimada K
Intern Med 2024 Apr 1;63(7):891-901. Epub 2023 Aug 23 doi: 10.2169/internalmedicine.2016-23. PMID: 37612088Free PMC Article
Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
O'Grady JG
Liver Transpl 2000 Nov;6(6 Suppl 2):S23-9. doi: 10.1053/jlts.2000.18687. PMID: 11084081

Recent clinical studies

Etiology

Zheng BH, Zhang C, Wan WZ, Sun WT, Cheng X, Ni XJ, Ni XL, Suo T, Liu H, Shen S, Liu HB
BMC Surg 2022 Jun 29;22(1):253. doi: 10.1186/s12893-022-01689-7. PMID: 35768809Free PMC Article
Nakaya M, Kurokawa R, Watadani T, Morisaka H, Higuchi M, Toda Y, Kunichika H, Kusakabe M, Okada Y, Ohgiya Y, Okada M, Anai H, Abe O, Minami M
Abdom Radiol (NY) 2022 Jun;47(6):1917-1928. Epub 2022 Apr 30 doi: 10.1007/s00261-022-03524-2. PMID: 35488897
Luchini C, Pelosi G, Scarpa A, Mattiolo P, Marchiori D, Maragliano R, Sessa F, Uccella S
Pathologica 2021 Feb;113(1):28-38. doi: 10.32074/1591-951X-231. PMID: 33686308Free PMC Article
Tomaipitinca L, Mandatori S, Mancinelli R, Giulitti F, Petrungaro S, Moresi V, Facchiano A, Ziparo E, Gaudio E, Giampietri C
Nutrients 2019 Apr 11;11(4) doi: 10.3390/nu11040827. PMID: 30979078Free PMC Article
Hong N, Kim HJ, Byun JH, Kim SY, Kim KW, Kim JH, Hong SM
Abdom Imaging 2015 Jan;40(1):181-91. doi: 10.1007/s00261-014-0191-0. PMID: 25008023

Diagnosis

Jevdokimov D, Tauvena E, Jevdokimova N, Vilisova S, Kriviča O, Briede I, Tone T, Staka A, Gerina-Berzina A, Ozolins A, Pukitis A
Am J Case Rep 2023 Jun 21;24:e939239. doi: 10.12659/AJCR.939239. PMID: 37340629Free PMC Article
Han B, Seo YJ, Oh GH, You GR, Ma KY, Kim KH, Noh MG, Joo YE
Korean J Gastroenterol 2023 Mar 25;81(3):121-124. doi: 10.4166/kjg.2023.005. PMID: 36960694
Ishida M, Okano K, Sandoh K, Ito H, Ikeura T, Mitsuyama T, Miyoshi H, Shimatani M, Takaoka M, Okazaki K, Tsuta K
Diagn Cytopathol 2020 Feb;48(2):154-158. Epub 2019 Nov 7 doi: 10.1002/dc.24334. PMID: 31697402
Umezaki N, Hashimoto D, Yamashita YI, Nakagawa S, Nakao Y, Itoyama R, Yusa T, Yamao T, Okabe H, Imai K, Hayashi H, Chikamoto A, Baba H
Anticancer Res 2019 Feb;39(2):903-907. doi: 10.21873/anticanres.13192. PMID: 30711974
Michalopoulos N, Papavramidis TS, Karayannopoulou G, Pliakos I, Papavramidis ST, Kanellos I
Pathol Oncol Res 2014 Oct;20(4):765-75. Epub 2014 Jun 11 doi: 10.1007/s12253-014-9808-4. PMID: 24917351

Therapy

Odufalu FD, Zubairu J, Silverman W
BMJ Case Rep 2018 Sep 4;2018 doi: 10.1136/bcr-2017-221895. PMID: 30181397Free PMC Article
Fukasawa H, Tounou S, Nabetani M, Michida T
Intern Med 2017;56(5):499-503. Epub 2017 Mar 1 doi: 10.2169/internalmedicine.56.7520. PMID: 28250294Free PMC Article
Ravaioli M, Ercolani G, Neri F, Cescon M, Stacchini G, Del Gaudio M, Cucchetti A, Pinna AD
World J Gastroenterol 2014 May 14;20(18):5345-52. doi: 10.3748/wjg.v20.i18.5345. PMID: 24833864Free PMC Article
Snady H
Hematol Oncol Clin North Am 2002 Feb;16(1):53-79. doi: 10.1016/s0889-8588(01)00010-7. PMID: 12063829
Welch CE
N Engl J Med 1969 Feb 20;280(8):419-25 contd. doi: 10.1056/NEJM196902202800805. PMID: 4883944

Prognosis

Karam E, Hollenbach M, Abou Ali E, Auriemma F, Anderloni A, Barbier L, Belfiori G, Caillol F, Crippa S, Del Chiaro M, De Ponthaud C, Dahel Y, Falconi M, Giovannini M, Heling D, Inoue Y, Jarnagin WR, Leung G, Lupinacci RM, Mariani A, Masaryk V, Miksch RC, Musquer N, Napoleon B, Oba A, Partelli S, Petrone MC, Prat F, Repici A, Sauvanet A, Salzmann K, Schattner MA, Schulick R, Schwarz L, Soares K, Souche FR, Truant S, Vaillant JC, Wang T, Wedi E, Werner J, Weismüller TJ, Wichmann D, Will U, Zaccari P, Gulla A, Heise C, Regner S, Gaujoux S; Pancreas 2000 Research Group
Neuroendocrinology 2023;113(10):1024-1034. Epub 2023 Jun 27 doi: 10.1159/000531712. PMID: 37369186
Zheng BH, Zhang C, Wan WZ, Sun WT, Cheng X, Ni XJ, Ni XL, Suo T, Liu H, Shen S, Liu HB
BMC Surg 2022 Jun 29;22(1):253. doi: 10.1186/s12893-022-01689-7. PMID: 35768809Free PMC Article
Kiya Y, Nagakawa Y, Takishita C, Osakabe H, Nishino H, Akashi M, Yamaguchi H, Nagao T, Oono R, Katsumata K, Tsuchida A
BMC Gastroenterol 2021 Jun 12;21(1):257. doi: 10.1186/s12876-021-01777-7. PMID: 34118881Free PMC Article
Zhang L, Wan D, Bao L, Chen Q, Xie H, Xu S, Lin S
Medicine (Baltimore) 2018 Jul;97(29):e11487. doi: 10.1097/MD.0000000000011487. PMID: 30024526Free PMC Article
Michalopoulos N, Papavramidis TS, Karayannopoulou G, Pliakos I, Papavramidis ST, Kanellos I
Pathol Oncol Res 2014 Oct;20(4):765-75. Epub 2014 Jun 11 doi: 10.1007/s12253-014-9808-4. PMID: 24917351

Clinical prediction guides

Luchini C, Scarpa A
Hum Pathol 2023 Feb;132:176-182. Epub 2022 Jun 14 doi: 10.1016/j.humpath.2022.06.009. PMID: 35714836
Zheng BH, Zhang C, Wan WZ, Sun WT, Cheng X, Ni XJ, Ni XL, Suo T, Liu H, Shen S, Liu HB
BMC Surg 2022 Jun 29;22(1):253. doi: 10.1186/s12893-022-01689-7. PMID: 35768809Free PMC Article
Okura K, Esaki M, Nara S, Ban D, Takamoto T, Shimada K, Hiraoka N
Pathol Int 2022 Jun;72(6):332-342. Epub 2022 Apr 26 doi: 10.1111/pin.13226. PMID: 35472251
Kiya Y, Nagakawa Y, Takishita C, Osakabe H, Nishino H, Akashi M, Yamaguchi H, Nagao T, Oono R, Katsumata K, Tsuchida A
BMC Gastroenterol 2021 Jun 12;21(1):257. doi: 10.1186/s12876-021-01777-7. PMID: 34118881Free PMC Article
Hong N, Kim HJ, Byun JH, Kim SY, Kim KW, Kim JH, Hong SM
Abdom Imaging 2015 Jan;40(1):181-91. doi: 10.1007/s00261-014-0191-0. PMID: 25008023

Recent systematic reviews

Ziogas IA, Rallis KS, Tasoudis PT, Moris D, Schulick RD, Del Chiaro M
Eur J Surg Oncol 2023 Apr;49(4):682-687. Epub 2023 Jan 9 doi: 10.1016/j.ejso.2023.01.005. PMID: 36646615
Giannakodimos I, Giannakodimos A, Ziogou A, Frountzas M, Kritikos N, Vlachos K, Toutouzas KG, Schizas D
J Gastrointestin Liver Dis 2022 Dec 17;31(4):459-466. doi: 10.15403/jgld-4383. PMID: 36535044
Beger HG, Mayer B, Rau BM
J Gastrointest Surg 2016 Jan;20(1):206-17. Epub 2015 Nov 2 doi: 10.1007/s11605-015-2981-2. PMID: 26525207
Beger HG, Nakao A, Mayer B, Poch B
Pancreatology 2015 Mar-Apr;15(2):167-78. Epub 2015 Feb 7 doi: 10.1016/j.pan.2015.01.009. PMID: 25732271
Michalopoulos N, Papavramidis TS, Karayannopoulou G, Pliakos I, Papavramidis ST, Kanellos I
Pathol Oncol Res 2014 Oct;20(4):765-75. Epub 2014 Jun 11 doi: 10.1007/s12253-014-9808-4. PMID: 24917351

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