Diffuse Large B-Cell Lymphoma Arising in HHV8-Positive Multicentric Castleman Disease

MedGen UID:: 758641
•Concept ID:: C3472615
•: Neoplastic Process

Synonyms:

Kaposi Sarcoma-Associated Human Herpes Virus 8 Positive Extracavity Lymphoma; Kaposi's Sarcoma-Associated Human Herpes Virus 8 Positive Extracavity Lymphoma; Kaposi's Sarcoma-Associated Human Herpes Virus 8+ Extracavity Lymphoma; KSHV-Associated Non-Hodgkin Lymphoma; Large B-Cell Lymphoma Arising in HHV 8-Associated Multicentric Castleman Disease; Large B-cell lymphoma arising in HHV8 associated multicentric Castleman disease; Large B-Cell Lymphoma Arising in HHV8-Associated Multicentric Castleman Disease; Large B-cell lymphoma arising in HHV8-associated multicentric Castleman disease; Large B-Cell Lymphoma Arising in Human Herpes Virus 8-Associated Multicentric Castleman Disease; Large B-cell lymphoma arising in human herpesvirus type 8 associated multicentric Castleman disease

SNOMED CT:

Large B-cell lymphoma arising in human herpesvirus type 8 associated multicentric Castleman disease (450911001); Large B-cell lymphoma arising in HHV8 associated multicentric Castleman disease (450911001); Large B-cell lymphoma arising in HHV8-associated multicentric Castleman disease (866098005)

Definition

An aggressive diffuse large B-cell lymphoma occurring in patients with HHV8-positive multicentric Castleman disease. It is characterized by the presence of human herpesvirus 8-infected large B-lymphocytes that resemble plasmablasts. It is usually seen in patients with HIV infection. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVDiffuse Large B-Cell Lymphoma Arising in HHV8-Positive Multicentric Castleman Disease

Disease
- Disorder by Site
  - Hematopoietic and Lymphoid System Disorder
    - Hematologic disorder
      - Lymphoproliferative disorder
        HHV8-Related Lymphoproliferative Disorder
        Diffuse Large B-Cell Lymphoma Arising in HHV8-Positive Multicentric Castleman Disease
        AIDS-Related Diffuse Large B-Cell Lymphoma Arising in HHV8-Positive Multicentric Castleman Disease

Recent clinical studies

Etiology

Demographic characteristics and prognosis of HHV8-positive diffuse large B-cell lymphoma, not otherwise specified: Insights from a population-based study with a 10-year follow-up.

Wang F, Du Z
Medicine (Baltimore) 2023 Dec 15;102(50):e36464. doi: 10.1097/MD.0000000000036464. PMID: 38115350 Free PMC Article

See all (1)

Diagnosis

Demographic characteristics and prognosis of HHV8-positive diffuse large B-cell lymphoma, not otherwise specified: Insights from a population-based study with a 10-year follow-up.

Wang F, Du Z
Medicine (Baltimore) 2023 Dec 15;102(50):e36464. doi: 10.1097/MD.0000000000036464. PMID: 38115350 Free PMC Article

See all (1)

Prognosis

Demographic characteristics and prognosis of HHV8-positive diffuse large B-cell lymphoma, not otherwise specified: Insights from a population-based study with a 10-year follow-up.

Wang F, Du Z
Medicine (Baltimore) 2023 Dec 15;102(50):e36464. doi: 10.1097/MD.0000000000036464. PMID: 38115350 Free PMC Article

See all (1)

Clinical prediction guides

Demographic characteristics and prognosis of HHV8-positive diffuse large B-cell lymphoma, not otherwise specified: Insights from a population-based study with a 10-year follow-up.

Wang F, Du Z
Medicine (Baltimore) 2023 Dec 15;102(50):e36464. doi: 10.1097/MD.0000000000036464. PMID: 38115350 Free PMC Article

See all (1)

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Diffuse Large B-Cell Lymphoma Arising in HHV8-Positive Multicentric Castleman Disease

Definition

Term Hierarchy

Recent clinical studies

Etiology

Diagnosis

Prognosis

Clinical prediction guides

Supplemental Content

Table of contents

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