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Corticotropin-releasing hormone deficient adrenal insufficiency

MedGen UID:
866776
Concept ID:
C4021127
Disease or Syndrome
Synonyms: Corticotropin-Releasing Hormone Deficiency; CRH deficient adrenal insufficiency; Tertiary adrenal insufficiency
 
HPO: HP:0011737

Definition

Adrenal insufficiency secondary to a defect in corticotropin-releasing hormone production. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCorticotropin-releasing hormone deficient adrenal insufficiency

Professional guidelines

PubMed

Woodcock T, Barker P, Daniel S, Fletcher S, Wass JAH, Tomlinson JW, Misra U, Dattani M, Arlt W, Vercueil A
Anaesthesia 2020 May;75(5):654-663. Epub 2020 Feb 3 doi: 10.1111/anae.14963. PMID: 32017012
Paragliola RM, Corsello SM
Minerva Endocrinol 2018 Jun;43(2):183-197. Epub 2017 Jul 27 doi: 10.23736/S0391-1977.17.02701-8. PMID: 28750490
Ouleghzal H, Rosales C, Raffin-Sanson ML
Ann Endocrinol (Paris) 2012 Feb;73(1):12-9. Epub 2012 Feb 10 doi: 10.1016/j.ando.2012.01.001. PMID: 22325371

Recent clinical studies

Etiology

Woodcock T, Barker P, Daniel S, Fletcher S, Wass JAH, Tomlinson JW, Misra U, Dattani M, Arlt W, Vercueil A
Anaesthesia 2020 May;75(5):654-663. Epub 2020 Feb 3 doi: 10.1111/anae.14963. PMID: 32017012
Paragliola RM, Corsello SM
Minerva Endocrinol 2018 Jun;43(2):183-197. Epub 2017 Jul 27 doi: 10.23736/S0391-1977.17.02701-8. PMID: 28750490
Webb EA, Krone N
Best Pract Res Clin Endocrinol Metab 2015 Jun;29(3):449-68. Epub 2015 Apr 22 doi: 10.1016/j.beem.2015.04.002. PMID: 26051302
Merke DP, Bornstein SR, Avila NA, Chrousos GP
Ann Intern Med 2002 Feb 19;136(4):320-34. doi: 10.7326/0003-4819-136-4-200202190-00012. PMID: 11848730
Schulte HM, Chrousos GP, Avgerinos P, Oldfield EH, Gold PW, Cutler GB Jr, Loriaux DL
J Clin Endocrinol Metab 1984 Jun;58(6):1064-7. doi: 10.1210/jcem-58-6-1064. PMID: 6327750

Diagnosis

Paragliola RM, Corsello SM
Minerva Endocrinol 2018 Jun;43(2):183-197. Epub 2017 Jul 27 doi: 10.23736/S0391-1977.17.02701-8. PMID: 28750490
El-Farhan N, Rees DA, Evans C
Ann Clin Biochem 2017 May;54(3):308-322. Epub 2017 Mar 16 doi: 10.1177/0004563216687335. PMID: 28068807
de Miguel Novoa P, Vela ET, García NP, Rodríguez MM, Guerras IS, Martínez de Salinas Santamaría Mde L, Masó AA; Área de Conocimiento del Grupo de Neuroendocrino de la SEEN (Grupo Insuficiencia Adrenal)
Endocrinol Nutr 2014 Sep;61 Suppl 1:1-35. doi: 10.1016/S1575-0922(14)73526-0. PMID: 25128212
Ouleghzal H, Rosales C, Raffin-Sanson ML
Ann Endocrinol (Paris) 2012 Feb;73(1):12-9. Epub 2012 Feb 10 doi: 10.1016/j.ando.2012.01.001. PMID: 22325371
Moraes RB, Czepielewski MA, Friedman G, Borba EL
Arq Bras Endocrinol Metabol 2011 Jun;55(5):295-302. doi: 10.1590/s0004-27302011000500001. PMID: 21881811

Therapy

Dreves B, Reznik Y, Tabarin A
Ann Endocrinol (Paris) 2023 Aug;84(4):472-480. Epub 2023 Feb 25 doi: 10.1016/j.ando.2023.01.008. PMID: 36842612
Woodcock T, Barker P, Daniel S, Fletcher S, Wass JAH, Tomlinson JW, Misra U, Dattani M, Arlt W, Vercueil A
Anaesthesia 2020 May;75(5):654-663. Epub 2020 Feb 3 doi: 10.1111/anae.14963. PMID: 32017012
Paragliola RM, Corsello SM
Minerva Endocrinol 2018 Jun;43(2):183-197. Epub 2017 Jul 27 doi: 10.23736/S0391-1977.17.02701-8. PMID: 28750490
Webb EA, Krone N
Best Pract Res Clin Endocrinol Metab 2015 Jun;29(3):449-68. Epub 2015 Apr 22 doi: 10.1016/j.beem.2015.04.002. PMID: 26051302
Moraes RB, Czepielewski MA, Friedman G, Borba EL
Arq Bras Endocrinol Metabol 2011 Jun;55(5):295-302. doi: 10.1590/s0004-27302011000500001. PMID: 21881811

Prognosis

Namikawa T, Shimizu S, Yokota K, Tanioka N, Fukudome I, Munekage M, Uemura S, Maeda H, Kitagawa H, Hanazaki K
Clin J Gastroenterol 2021 Aug;14(4):988-993. Epub 2021 Mar 14 doi: 10.1007/s12328-021-01384-9. PMID: 33715100
Sakao Y, Sugiura T, Tsuji T, Ohashi N, Yasuda H, Fujigaki Y, Kato A
Intern Med 2014;53(14):1485-90. Epub 2014 Jul 15 doi: 10.2169/internalmedicine.53.1104. PMID: 25030558
Naing KK, Dewar JA, Leese GP
Cancer 1999 Sep 15;86(6):1044-9. PMID: 10491532
Fukata J, Shimizu N, Imura H, Hibi I, Tanaka K, Tanaka T, Nakagawa S, Takebe K, Kimura K, Yoshinaga K
Endocr J 1993 Oct;40(5):597-606. doi: 10.1507/endocrj.40.597. PMID: 7951526
Müller OA, Stalla GK, von Werder K
Horm Res 1987;25(4):185-98. doi: 10.1159/000180652. PMID: 3034758

Clinical prediction guides

Yamamoto M, Ben-Shlomo A, Kameda H, Fukuoka H, Deng N, Ding Y, Melmed S
JCI Insight 2018 Oct 4;3(19) doi: 10.1172/jci.insight.122932. PMID: 30282821Free PMC Article
El-Farhan N, Rees DA, Evans C
Ann Clin Biochem 2017 May;54(3):308-322. Epub 2017 Mar 16 doi: 10.1177/0004563216687335. PMID: 28068807
Lin SY, Won JG, Lee TI, Tang KT, Lin HD
Zhonghua Yi Xue Za Zhi (Taipei) 2002 Apr;65(4):156-63. PMID: 12135194
Fukata J, Shimizu N, Imura H, Hibi I, Tanaka K, Tanaka T, Nakagawa S, Takebe K, Kimura K, Yoshinaga K
Endocr J 1993 Oct;40(5):597-606. doi: 10.1507/endocrj.40.597. PMID: 7951526
Müller OA, Stalla GK, von Werder K
Horm Res 1987;25(4):185-98. doi: 10.1159/000180652. PMID: 3034758

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