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Supracardiac total anomalous pulmonary venous connection

MedGen UID:
866780
•Concept ID:
C4021131
•
Anatomical Abnormality
Synonyms: Supracardiac total anomalous pulmonary venous connexion; Total anomalous pulmonary venous connection, supracardiac; Type 1 total anomalous pulmonary venous connection
 
HPO: HP:0011719

Definition

Type 1 total anomalous pulmonary venous connection. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSupracardiac total anomalous pulmonary venous connection

Professional guidelines

PubMed

Prenatal diagnosis of total anomalous pulmonary venous connection using 2D and HDlive flow combined with spatiotemporal image correlation.
Li TG, Ma B, Gao YH, Zhang RH, Li PL, Da ZQ
Echocardiography 2022 Oct;39(10):1269-1275. Epub 2022 Sep 13 doi: 10.1111/echo.15429. PMID: 36100867
Single Ventricle and Total Anomalous Pulmonary Venous Connection: Implications of Prenatal Diagnosis.
Hancock HS, Romano JC, Armstrong A, Yu S, Lowery R, Gelehrter S
World J Pediatr Congenit Heart Surg 2018 Jul;9(4):434-439. doi: 10.1177/2150135118771344. PMID: 29945508
Prenatal findings in total anomalous pulmonary venous return: a diagnostic road map starts with obstetric screening views.
Ganesan S, Brook MM, Silverman NH, Moon-Grady AJ
J Ultrasound Med 2014 Jul;33(7):1193-207. doi: 10.7863/ultra.33.7.1193. PMID: 24958406

Recent clinical studies

Etiology

Modified L-shaped incision technique for supracardiac total anomalous pulmonary venous connection as an alternative to sutureless technique.
Feng Z, He Q, Yuan J, Dou Z, Wu D, Liu Y, Rui L, He F, Wu Z, Li S
Int J Surg 2023 Dec 1;109(12):3788-3795. doi: 10.1097/JS9.0000000000000694. PMID: 37678273Free PMC Article
Supracardiac total anomalous pulmonary venous connection type Ib: Morphology and outcomes.
Liu X, Liufu R, Liu T, Cen J, Yu J, Wen S, Ou Y, Chen J, Zhuang J
J Thorac Cardiovasc Surg 2023 Jul;166(1):193-200.e1. Epub 2022 Oct 14 doi: 10.1016/j.jtcvs.2022.10.008. PMID: 36732145
A Modified Approach with Caval Transection for Supracardiac Total Anomalous Pulmonary Venous Connection: Comparison Between Conventional and Sutureless Surgery in 173 Patients.
Qiu ZH, Liao LM, Xiao J, Chen XF, Liao DS, Tang MR, Wu QS, Xie XB, Zhu YP, Chen LW
Pediatr Cardiol 2021 Jun;42(5):1002-1009. Epub 2021 Mar 23 doi: 10.1007/s00246-021-02573-6. PMID: 33759021
Early and Intermediate-Term Results for the Combined Superior Approach Correction of Supracardiac Total Anomalous Pulmonary Venous Connection in Neonatal Patients.
Sui R, Zi J, Li D, Li Q, Wang A
Heart Lung Circ 2021 Aug;30(8):1256-1262. Epub 2021 Mar 13 doi: 10.1016/j.hlc.2021.01.008. PMID: 33722488
Superior Approach for Supracardiac Total Anomalous Pulmonary Venous Connection.
Liufu R, Shi G, Zhu F, Guan Y, Lu Z, Chen W, Zhu Z, Chen H
Ann Thorac Surg 2018 May;105(5):1429-1435. Epub 2018 Feb 15 doi: 10.1016/j.athoracsur.2018.01.039. PMID: 29454717

Diagnosis

Supracardiac total anomalous pulmonary venous connection type Ib: Morphology and outcomes.
Liu X, Liufu R, Liu T, Cen J, Yu J, Wen S, Ou Y, Chen J, Zhuang J
J Thorac Cardiovasc Surg 2023 Jul;166(1):193-200.e1. Epub 2022 Oct 14 doi: 10.1016/j.jtcvs.2022.10.008. PMID: 36732145
Fetal case of rare association of hypoplastic left heart syndrome and absent atrial septum accompanied by mixed form of supracardiac total anomalous pulmonary venous connection.
Maruyama W, Kawasaki Y, Murakami Y, Fujino M, Sasaki T, Nakamura K, Ehara E
Echocardiography 2022 Feb;39(2):375-380. Epub 2022 Jan 6 doi: 10.1111/echo.15272. PMID: 34994012
Supracardiac total anomalous pulmonary venous connection with cor triatriatum sinister: A rare diagnosis confirmed by saline contrast echocardiography.
Relan J, Choubey M, Kothari SS
Echocardiography 2020 Dec;37(12):2168-2170. Epub 2020 Oct 27 doi: 10.1111/echo.14914. PMID: 33107635
Prenatal diagnoses of an uncommon isolated obstructed supracardiac total anomalous pulmonary venous connection: Case report and review of the literature (CARE compliant).
Muntean I, Mărginean C, Stanca R, Togănel R, Pop M, Gozar L
Medicine (Baltimore) 2017 Feb;96(5):e6061. doi: 10.1097/MD.0000000000006061. PMID: 28151919Free PMC Article
Supracardiac total anomalous pulmonary venous connection with bilateral (right and left) vertical veins and bilateral obstruction.
Gavali SA, Phadke MS, Kerkar PG
Pediatr Cardiol 2013 Oct;34(7):1751-3. Epub 2013 Jan 25 doi: 10.1007/s00246-013-0641-4. PMID: 23354149

Therapy

A Modified Approach with Caval Transection for Supracardiac Total Anomalous Pulmonary Venous Connection: Comparison Between Conventional and Sutureless Surgery in 173 Patients.
Qiu ZH, Liao LM, Xiao J, Chen XF, Liao DS, Tang MR, Wu QS, Xie XB, Zhu YP, Chen LW
Pediatr Cardiol 2021 Jun;42(5):1002-1009. Epub 2021 Mar 23 doi: 10.1007/s00246-021-02573-6. PMID: 33759021
Modified "sutureless" anastomosis for primary repair of supracardiac total anomalous pulmonary venous connection.
Suarez MR, Panos AL, Salerno TA, Ricci M
J Card Surg 2009 Sep-Oct;24(5):564-6. doi: 10.1111/j.1540-8191.2009.00886.x. PMID: 19740299
Visualization of pulmonary vein obstruction by pulmonary artery wedge injection and documentation by pressure tracings: report of one case with persistent wheezing following correction of total anomalous pulmonary venous connection.
Lee ML, Wang JK, Lue HC
Int J Cardiol 1995 Apr;49(2):167-72. doi: 10.1016/0167-5273(95)02277-4. PMID: 7628888
Successful balloon dilatation of ascending vein stenosis in obstructed supracardiac total anomalous pulmonary venous connection.
Bu'Lock FA, Jordan SC, Martin RP
Pediatr Cardiol 1994 Mar-Apr;15(2):78-80. doi: 10.1007/BF00817612. PMID: 7527911

Prognosis

Supracardiac total anomalous pulmonary venous connection type Ib: Morphology and outcomes.
Liu X, Liufu R, Liu T, Cen J, Yu J, Wen S, Ou Y, Chen J, Zhuang J
J Thorac Cardiovasc Surg 2023 Jul;166(1):193-200.e1. Epub 2022 Oct 14 doi: 10.1016/j.jtcvs.2022.10.008. PMID: 36732145
Repair of a mixed form of supracardiac total anomalous pulmonary venous connection.
Kawasaki Y, Dentel JN, Walters HL, Galas JM, Kobayashi D
Cardiol Young 2021 Feb;31(2):300-302. Epub 2020 Nov 3 doi: 10.1017/S1047951120003625. PMID: 33140713
Superior Approach for Supracardiac Total Anomalous Pulmonary Venous Connection.
Liufu R, Shi G, Zhu F, Guan Y, Lu Z, Chen W, Zhu Z, Chen H
Ann Thorac Surg 2018 May;105(5):1429-1435. Epub 2018 Feb 15 doi: 10.1016/j.athoracsur.2018.01.039. PMID: 29454717
Supracardiac total anomalous pulmonary venous connection with bilateral (right and left) vertical veins and bilateral obstruction.
Gavali SA, Phadke MS, Kerkar PG
Pediatr Cardiol 2013 Oct;34(7):1751-3. Epub 2013 Jan 25 doi: 10.1007/s00246-013-0641-4. PMID: 23354149
Modified anastomosis for repair of supracardiac total anomalous pulmonary venous connection in infants.
Ou-Yang WB, Zhang H, Yang KM, Li SJ
J Card Surg 2012 May;27(3):387-9. Epub 2012 Apr 23 doi: 10.1111/j.1540-8191.2012.01448.x. PMID: 22519526

Clinical prediction guides

Modified L-shaped incision technique for supracardiac total anomalous pulmonary venous connection as an alternative to sutureless technique.
Feng Z, He Q, Yuan J, Dou Z, Wu D, Liu Y, Rui L, He F, Wu Z, Li S
Int J Surg 2023 Dec 1;109(12):3788-3795. doi: 10.1097/JS9.0000000000000694. PMID: 37678273Free PMC Article
Fetal case of rare association of hypoplastic left heart syndrome and absent atrial septum accompanied by mixed form of supracardiac total anomalous pulmonary venous connection.
Maruyama W, Kawasaki Y, Murakami Y, Fujino M, Sasaki T, Nakamura K, Ehara E
Echocardiography 2022 Feb;39(2):375-380. Epub 2022 Jan 6 doi: 10.1111/echo.15272. PMID: 34994012
Total anomalous pulmonary venous connection mimicking hypoplastic left heart syndrome.
Matsuoka R, Muneuchi J, Ochiai Y
Cardiol Young 2021 Nov;31(11):1861-1863. Epub 2021 May 4 doi: 10.1017/S1047951121001670. PMID: 33941300
Mid-term results of modified L-shaped incision technique for supracardiac total anomalous pulmonary venous connection.
Feng Z, Yang Y, He F, Pang K, Ma K, Zhang S, Qi L, Wang G, Mao F, Yuan J, Li S
Eur J Cardiothorac Surg 2020 Dec 1;58(6):1261-1268. doi: 10.1093/ejcts/ezaa264. PMID: 32888293
Dysphonia: a frequently encountered symptom in the evaluation of infants with unobstructed supracardiac total anomalous pulmonary venous connection.
Shankargouda S, Krishnan U, Murali R, Shah MJ
Pediatr Cardiol 2000 Sep-Oct;21(5):458-60. doi: 10.1007/s002460010108. PMID: 10982706

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