Generalized microdontia

MedGen UID:: 870614
•Concept ID:: C4025065
•: Finding

Synonyms:	Decreased size of all teeth; Decreased tooth mass; Decreased width of all teeth; Generalised microdontia; Hypotrophy of all teeth; Tooth mass insufficiency

HPO:	HP:0006311

Definition

A generalized form of microdontia. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVGeneralized microdontia

Abnormality of the mouth
- Abnormal oral morphology
  - Abnormal oral cavity morphology
    - Abnormality of the dentition
      - Abnormal dental morphology
        Microdontia
        Generalized microdontia

Conditions with this feature

Amelogenesis imperfecta type 1A

MedGen UID:: 859840
•Concept ID:: C4011403
•: Disease or Syndrome

Hypoplastic amelogenesis imperfecta IA is characterized by enamel that may not develop to normal thickness. The enamel may have pits on the labial or buccal surfaces that are often arranged in rows and columns (see Witkop, 1989).

See: Condition Record

Amelogenesis imperfecta type 1A

Professional guidelines

PubMed

Dental management of Rapp-Hodgkin syndrome associated with oral cleft and hypodontia.

Karthikeyani S, Thirumurthy VR, Yuvaraja BA
J Indian Soc Pedod Prev Dent 2016 Apr-Jun;34(2):192-5. doi: 10.4103/0970-4388.180453. PMID: 27080974

Cervico-facial irradiation and orthodontic treatment.

Elhaddaoui R, Bahije L, Chbicheb S, Zaoui F
Int Orthod 2015 Jun;13(2):139-148. Epub 2015 May 16 doi: 10.1016/j.ortho.2015.03.017. PMID: 25986706

The oral health needs of children after treatment for a solid tumour or lymphoma.

Hutton A, Bradwell M, English M, Chapple I
Int J Paediatr Dent 2010 Jan;20(1):15-23. doi: 10.1111/j.1365-263X.2009.00999.x. PMID: 20059589

See all (3)

Recent clinical studies

Etiology

Oral and dental findings in children with Fanconi anemia.

Tekcicek M, Tavil B, Cakar A, Pinar A, Unal S, Gumruk F
Pediatr Dent 2007 May-Jun;29(3):248-52. PMID: 17688024

See all (1)

Diagnosis

Non-syndromic occurrence of true generalized microdontia with hypodontia: A case report.

Chen Y, Zhou F, Peng Y, Chen L, Wang Y
Medicine (Baltimore) 2019 Jun;98(26):e16283. doi: 10.1097/MD.0000000000016283. PMID: 31261601 Free PMC Article

CANDLE Syndrome: orodfacial manifestations and dental implications.

Roberts T, Stephen L, Scott C, di Pasquale T, Naser-Eldin A, Chetty M, Shaik S, Lewandowski L, Beighton P
Head Face Med 2015 Dec 28;11:38. doi: 10.1186/s13005-015-0095-4. PMID: 26711936 Free PMC Article

Non-syndromic occurrence of true generalized microdontia with mandibular mesiodens - a rare case.

Bargale SD, Kiran SD
Head Face Med 2011 Oct 28;7:19. doi: 10.1186/1746-160X-7-19. PMID: 22035324 Free PMC Article

Novel mutations in GJA1 cause oculodentodigital syndrome.

Fenwick A, Richardson RJ, Butterworth J, Barron MJ, Dixon MJ
J Dent Res 2008 Nov;87(11):1021-6. doi: 10.1177/154405910808701108. PMID: 18946008 Free PMC Article

Oral and dental findings in children with Fanconi anemia.

Tekcicek M, Tavil B, Cakar A, Pinar A, Unal S, Gumruk F
Pediatr Dent 2007 May-Jun;29(3):248-52. PMID: 17688024

See all (7)