PGAP2 is essential for correct processing and stable expression of GPI-anchored proteins

Mol Biol Cell. 2006 Mar;17(3):1410-20. doi: 10.1091/mbc.e05-11-1005. Epub 2006 Jan 11.

Abstract

Biosynthesis of glycosylphosphatidylinositol-anchored proteins (GPI-APs) in the ER has been extensively studied, whereas the molecular events during the transport of GPI-APs from the ER to the cell surface are poorly understood. Here, we established new mutant cell lines whose surface expressions of GPI-APs were greatly decreased despite normal biosynthesis of GPI-APs in the ER. We identified a gene responsible for this defect, designated PGAP2 (for Post-GPI-Attachment to Proteins 2), which encoded a Golgi/ER-resident membrane protein. The low surface expression of GPI-APs was due to their secretion into the culture medium. GPI-APs were modified/cleaved by two reaction steps in the mutant cells. First, the GPI anchor was converted to lyso-GPI before exiting the trans-Golgi network. Second, lyso-GPI-APs were cleaved by a phospholipase D after transport to the plasma membrane. Therefore, PGAP2 deficiency caused transport to the cell surface of lyso-GPI-APs that were sensitive to a phospholipase D. These results demonstrate that PGAP2 is involved in the processing of GPI-APs required for their stable expression at the cell surface.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Animals
  • CD55 Antigens / metabolism
  • CD59 Antigens / metabolism
  • CHO Cells
  • Cell Membrane / metabolism
  • Cells, Cultured
  • Cloning, Molecular
  • Cricetinae
  • Cricetulus
  • Culture Media, Serum-Free
  • Endoplasmic Reticulum / metabolism
  • Glycosylphosphatidylinositols / biosynthesis
  • Glycosylphosphatidylinositols / chemistry
  • Glycosylphosphatidylinositols / metabolism*
  • Humans
  • Inositol / metabolism
  • Membrane Proteins / metabolism
  • Molecular Sequence Data
  • Mutation / genetics
  • Nuclear Proteins / genetics
  • Nuclear Proteins / metabolism*
  • Phosphates / metabolism
  • Protein Processing, Post-Translational*
  • Protein Transport
  • Rats

Substances

  • CD55 Antigens
  • CD59 Antigens
  • Culture Media, Serum-Free
  • Glycosylphosphatidylinositols
  • Membrane Proteins
  • Nuclear Proteins
  • PGAP2 protein, rat
  • Phosphates
  • Inositol