Congenital lung malformations: informing best practice

Semin Pediatr Surg. 2014 Oct;23(5):270-7. doi: 10.1053/j.sempedsurg.2014.09.007. Epub 2014 Sep 4.

Abstract

The management of congenital lung malformations is controversial both in the prenatal and postnatal periods. This article attempts to inform best practice by reviewing the level of evidence with regard to prenatal diagnosis, prognosis, and management and postnatal management, including imaging, surgical indication, surgical approach, and risk of malignancy. We present a series of clinically relevant statements along those topics and analyze the evidence for each. In the end, we make a plea for an adequate description of the lesions, both before and after birth, which will allow future comparisons between management options and the initiation of prospective registries.

Keywords: Congenital lung lesions; Congenital pulmonary airway malformations; Cystic adenomatoid malformation; Pleuropulmonary blastoma; Sequestration.

Publication types

  • Review

MeSH terms

  • Female
  • Fetal Diseases* / diagnosis
  • Fetal Diseases* / drug therapy
  • Fetal Diseases* / surgery
  • Humans
  • Infant, Newborn
  • Infant, Newborn, Diseases* / diagnosis
  • Infant, Newborn, Diseases* / drug therapy
  • Infant, Newborn, Diseases* / surgery
  • Lung Diseases* / congenital
  • Lung Diseases* / diagnosis
  • Lung Diseases* / drug therapy
  • Lung Diseases* / surgery
  • Practice Guidelines as Topic*
  • Pregnancy
  • Prenatal Diagnosis / methods*
  • Prenatal Diagnosis / standards
  • Respiratory System Abnormalities* / diagnosis
  • Respiratory System Abnormalities* / drug therapy
  • Respiratory System Abnormalities* / surgery