The first Moroccan case of severe type II congenital plasminogen deficiency with ligneous conjunctivitis

Ann Biol Clin (Paris). 2022 Feb 1;80(1):81-83. doi: 10.1684/abc.2022.1707.

Abstract

Ligneous conjunctivitis (LC) is a rare form of pseudomembranous chronic conjunctivitis caused by a deficiency in plasminogen activity. Due to its rarity, little is known about this disorder. We hereby report a case of ligneous conjunctivitis, describing the clinical findings, the biological diagnosis and the treatment of this rare disease.

Keywords: ligneous conjunctivitis; plasminogen deficiency; pseudomembranes; recurrence.

Publication types

  • Case Reports

MeSH terms

  • Coagulation Protein Disorders* / complications
  • Conjunctivitis* / diagnosis
  • Conjunctivitis* / drug therapy
  • Conjunctivitis* / etiology
  • Humans
  • Morocco
  • Plasminogen / deficiency
  • Plasminogen / therapeutic use
  • Skin Diseases, Genetic

Substances

  • Plasminogen

Supplementary concepts

  • Congenital Plasminogen Deficiency
  • Plasminogen Deficiency, Type I