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Factor X Inactivation

MedGen UID:
1375228
Concept ID:
C4329970
Disease or Syndrome

Definition

Presence of inactivating antibodies to factor X in the blood. [from NCI]

Professional guidelines

PubMed

Joseph BC, Miyazawa BY, Esmon CT, Cohen MJ, von Drygalski A, Mosnier LO
Blood Adv 2022 Feb 8;6(3):959-969. doi: 10.1182/bloodadvances.2021005257. PMID: 34861695Free PMC Article
Pescatore SL
Expert Opin Pharmacother 2001 Mar;2(3):431-9. doi: 10.1517/14656566.2.3.431. PMID: 11336597
Edwards CA, Piet MP, Chin S, Horowitz B
Vox Sang 1987;52(1-2):53-9. doi: 10.1111/j.1423-0410.1987.tb02989.x. PMID: 3111089

Recent clinical studies

Etiology

Kobayashi H, Matsubara S, Imanaka S
J Obstet Gynaecol Res 2023 Jul;49(7):1677-1683. Epub 2023 Apr 25 doi: 10.1111/jog.15660. PMID: 37186495
Yada K, Nogami K
Arterioscler Thromb Vasc Biol 2020 May;40(5):1148-1154. Epub 2020 Apr 2 doi: 10.1161/ATVBAHA.120.312919. PMID: 32237902
Castoldi E, Hackeng TM
Curr Opin Hematol 2008 Sep;15(5):529-36. doi: 10.1097/MOH.0b013e328309ec97. PMID: 18695379
Federici AB
Haematologica 2003 Jun;88(6):EREP02. PMID: 12826528
Nicolaes GA, Dahlbäck B
Arterioscler Thromb Vasc Biol 2002 Apr 1;22(4):530-8. doi: 10.1161/01.atv.0000012665.51263.b7. PMID: 11950687

Diagnosis

Thomassen MCLGD, Bouwens BRC, Wichapong K, Suylen DP, Bouwman FG, Hackeng TM, Koenen RR
J Thromb Haemost 2023 May;21(5):1214-1226. Epub 2023 Jan 28 doi: 10.1016/j.jtha.2023.01.017. PMID: 36716968
Nanjo S, Wu W, Karachaliou N, Blakely CM, Suzuki J, Chou YT, Ali SM, Kerr DL, Olivas VR, Shue J, Rotow J, Mayekar MK, Haderk F, Chatterjee N, Urisman A, Yeo JC, Skanderup AJ, Tan AC, Tam WL, Arrieta O, Hosomichi K, Nishiyama A, Yano S, Kirichok Y, Tan DS, Rosell R, Okimoto RA, Bivona TG
J Clin Invest 2022 Jul 1;132(13) doi: 10.1172/JCI145099. PMID: 35579943Free PMC Article
Yada K, Nogami K
Arterioscler Thromb Vasc Biol 2020 May;40(5):1148-1154. Epub 2020 Apr 2 doi: 10.1161/ATVBAHA.120.312919. PMID: 32237902
Castoldi E, Hackeng TM
Curr Opin Hematol 2008 Sep;15(5):529-36. doi: 10.1097/MOH.0b013e328309ec97. PMID: 18695379
Hoekema L, Nicolaes GA, Hemker HC, Tans G, Rosing J
Biochemistry 1997 Mar 18;36(11):3331-5. doi: 10.1021/bi9623284. PMID: 9116011

Therapy

Yada K, Nogami K
Arterioscler Thromb Vasc Biol 2020 May;40(5):1148-1154. Epub 2020 Apr 2 doi: 10.1161/ATVBAHA.120.312919. PMID: 32237902
Heo YA
Drugs 2018 Jul;78(10):1049-1055. doi: 10.1007/s40265-018-0940-4. PMID: 29926311Free PMC Article
Orfeo T, Elsman R, Gissel M, Mann KG, Butenas S
Haemophilia 2016 May;22(3):462-73. Epub 2016 Jan 29 doi: 10.1111/hae.12872. PMID: 26822998
Federici AB
Haematologica 2003 Jun;88(6):EREP02. PMID: 12826528
Perry MO
Am J Surg 1988 Feb;155(2):268-76. doi: 10.1016/s0002-9610(88)80712-8. PMID: 3277474

Prognosis

Calcaterra V, Chiricosta L, Mazzon E, Gugnandolo A, Alberti D, Maestri L, Meroni M, Vestri E, Verduci E, Dilillo D, Zuccotti G, Pelizzo G
Orphanet J Rare Dis 2021 Oct 29;16(1):455. doi: 10.1186/s13023-021-02093-9. PMID: 34715892Free PMC Article
de Laat-Kremers RMW, Yan Q, Ninivaggi M, de Maat M, de Laat B
Sci Rep 2020 Jul 27;10(1):12544. doi: 10.1038/s41598-020-69415-y. PMID: 32719370Free PMC Article
Seki K, Mizuno Y, Sakashita T, Nakano S, Tanno J, Okazaki Y, Muramatsu T, Nishimura S, Senbonmatsu T
J Pharmacol Sci 2017 Mar;133(3):156-161. Epub 2017 Feb 24 doi: 10.1016/j.jphs.2017.02.010. PMID: 28314697
Bravo MC, Orfeo T, Mann KG, Everse SJ
BMC Syst Biol 2012 May 20;6:45. doi: 10.1186/1752-0509-6-45. PMID: 22607732Free PMC Article
Barendsz-Janson AF, Muller AD, Lichtenbeld HH, Van Dam-Mieras MC, Hillen HF
Tumour Biol 1998;19(2):104-12. doi: 10.1159/000029980. PMID: 9486561

Clinical prediction guides

de Laat-Kremers RMW, Yan Q, Ninivaggi M, de Maat M, de Laat B
Sci Rep 2020 Jul 27;10(1):12544. doi: 10.1038/s41598-020-69415-y. PMID: 32719370Free PMC Article
Ellington TM
J Pharm Pract 2020 Aug;33(4):465-470. Epub 2019 Jan 6 doi: 10.1177/0897190018822556. PMID: 30614371
Steffel J, Lüscher TF, Tanner FC
Circulation 2006 Feb 7;113(5):722-31. doi: 10.1161/CIRCULATIONAHA.105.567297. PMID: 16461845
Hoekema L, Nicolaes GA, Hemker HC, Tans G, Rosing J
Biochemistry 1997 Mar 18;36(11):3331-5. doi: 10.1021/bi9623284. PMID: 9116011
Vehar GA, Davie EW
Biochemistry 1980 Feb 5;19(3):401-10. doi: 10.1021/bi00544a001. PMID: 7356933

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