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Primary Pulmonary Myxoid Sarcoma with EWSR1-CREB1 Fusion

MedGen UID:
1379179
•Concept ID:
C4518372
•
Neoplastic Process
Synonyms: Low-Grade Malignant Myxoid Endobronchial Tumor; Primary Pulmonary Myxoid Sarcoma; Primary Pulmonary Myxoid Sarcoma with EWSR1::CREB1 Fusion; Pulmonary myxoid sarcoma with EWSR1-CREB1 translocation; Pulmonary Myxoid Sarcoma with EWSR1-CREB1 Translocation
SNOMED CT: Pulmonary myxoid sarcoma with EWSR1-CREB1 translocation (734072005)

Definition

A sarcoma that arises from the lung. It is related to a bronchus and is often predominantly endobronchial. It is characterized by the proliferation of round and spindle cells within a myxoid stroma. It is associated with the presence of an EWSR1::CREB1 fusion gene. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrimary Pulmonary Myxoid Sarcoma with EWSR1-CREB1 Fusion

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