Full Report

Format

Full Report
Summary (Text)
Summary (XML)

Send to:

Choose Destination

File
Clipboard
Collections

Central Nervous System Solitary Fibrous Tumor, Grade 3

MedGen UID:: 1386137
•Concept ID:: C4331858
•: Neoplastic Process

Synonyms:

Central Nervous System Solitary Fibrous Tumor/Hemangiopericytoma, Grade 3; CNS Solitary Fibrous Tumor, Grade 3; CNS Solitary Fibrous Tumor/Hemangiopericytoma, Grade 3

Definition

A solitary fibrous tumor that arises from the central nervous system. It most often corresponds to the tumor previously diagnosed as anaplastic hemangiopericytoma. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVCentral Nervous System Solitary Fibrous Tumor, Grade 3

Disorder of nervous system
- Disorder of the central nervous system
  - Neoplasm of the central nervous system
    - Primary Central Nervous System Neoplasm
      - Central nervous system mesenchymal non-meningothelial tumor
        Central Nervous System Solitary Fibrous Tumor
        Central Nervous System Solitary Fibrous Tumor, Grade 3
        Adult intracranial malignant hemangiopericytoma
        Meningeal Central Nervous System Solitary Fibrous Tumor, Grade 3

Professional guidelines

PubMed

Immunohistochemical Approach to the Differential Diagnosis of Meningiomas and Their Mimics.

Boulagnon-Rombi C, Fleury C, Fichel C, Lefour S, Marchal Bressenot A, Gauchotte G
J Neuropathol Exp Neurol 2017 Apr 1;76(4):289-298. doi: 10.1093/jnen/nlx008. PMID: 28340171

See all (1)

Recent clinical studies

Etiology

Clinical outcomes in central nervous system solitary-fibrous tumor/hemangiopericytoma: a STROBE-compliant single-center analysis.

Yu Y, Hu Y, Lv L, Chen C, Yin S, Jiang S, Zhou P
World J Surg Oncol 2022 May 10;20(1):149. doi: 10.1186/s12957-022-02619-w. PMID: 35538540 Free PMC Article

Solitary fibrous tumor of thoracic cavity, extra-thoracic sites and central nervous system: Clinicopathologic features and association with local recurrence and metastasis.

Alexiev BA, Finkelman BS, Streich L, Bautista MM, Pollack SM, Jennings LJ, Brat DJ
Pathol Res Pract 2021 Aug;224:153531. Epub 2021 Jun 18 doi: 10.1016/j.prp.2021.153531. PMID: 34171600

Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.

Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676

Hemangiopericytoma/Solitary Fibrous Tumor in the central nervous system. Experience with surgery and radiotherapy as a complementary treatment: A 10-year analysis of a heterogeneous series in a single tertiary center.

González-Vargas PM, Thenier-Villa JL, Sanromán Álvarez P, Serantes Combo A, Calero Félix L, Galárraga Campoverde RA, Azevedo González E, Martín-Gallego Á, Martínez-Rolan R, de la Lama Zaragoza A, Conde Alonso C
Neurocirugia (Astur : Engl Ed) 2020 Jan-Feb;31(1):14-23. Epub 2019 Jul 24 doi: 10.1016/j.neucir.2019.06.001. PMID: 31351895

Pathological prognostic markers in central nervous system solitary fibrous tumour/hemangiopericytoma: Evidence from a small series.

Bertero L, Anfossi V, Osella-Abate S, Disanto MG, Mantovani C, Zenga F, Rudà R, Garbossa D, Soffietti R, Ricardi U, Papotti M, Cassoni P
PLoS One 2018;13(9):e0203570. Epub 2018 Sep 5 doi: 10.1371/journal.pone.0203570. PMID: 30183767 Free PMC Article

See all (12)

Diagnosis

Meningioma and Other Meningeal Tumors.

Bailo M, Gagliardi F, Boari N, Spina A, Piloni M, Castellano A, Mortini P
Adv Exp Med Biol 2023;1405:73-97. doi: 10.1007/978-3-031-23705-8_3. PMID: 37452935

Solitary fibrous tumor of thoracic cavity, extra-thoracic sites and central nervous system: Clinicopathologic features and association with local recurrence and metastasis.

Alexiev BA, Finkelman BS, Streich L, Bautista MM, Pollack SM, Jennings LJ, Brat DJ
Pathol Res Pract 2021 Aug;224:153531. Epub 2021 Jun 18 doi: 10.1016/j.prp.2021.153531. PMID: 34171600

Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.

Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676

Pathological prognostic markers in central nervous system solitary fibrous tumour/hemangiopericytoma: Evidence from a small series.

Solitary fibrous tumours and haemangiopericytoma of the meninges. A retrospective study for outcome and prognostic factor assessment.

Champeaux C, Rousseau P, Devaux B, Nataf F, Tauziède-Espariat A
Neurochirurgie 2018 Mar;64(1):37-43. Epub 2018 Feb 21 doi: 10.1016/j.neuchi.2017.10.004. PMID: 29475608

See all (13)

Prognosis

Meningioma and Other Meningeal Tumors.

Bailo M, Gagliardi F, Boari N, Spina A, Piloni M, Castellano A, Mortini P
Adv Exp Med Biol 2023;1405:73-97. doi: 10.1007/978-3-031-23705-8_3. PMID: 37452935

Clinical outcomes in central nervous system solitary-fibrous tumor/hemangiopericytoma: a STROBE-compliant single-center analysis.

Yu Y, Hu Y, Lv L, Chen C, Yin S, Jiang S, Zhou P
World J Surg Oncol 2022 May 10;20(1):149. doi: 10.1186/s12957-022-02619-w. PMID: 35538540 Free PMC Article

Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.

Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676

Pathological prognostic markers in central nervous system solitary fibrous tumour/hemangiopericytoma: Evidence from a small series.

See all (12)

Clinical prediction guides

Solitary fibrous tumor of thoracic cavity, extra-thoracic sites and central nervous system: Clinicopathologic features and association with local recurrence and metastasis.

Alexiev BA, Finkelman BS, Streich L, Bautista MM, Pollack SM, Jennings LJ, Brat DJ
Pathol Res Pract 2021 Aug;224:153531. Epub 2021 Jun 18 doi: 10.1016/j.prp.2021.153531. PMID: 34171600

Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.

Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676

Solitary fibrous tumor/hemangiopericytoma in the cerebellopontine angle mimicking vestibular schwannoma: A case report and literature review.

Yue X, Huang J, Zhu Y, Du Y
Medicine (Baltimore) 2020 Mar;99(13):e19651. doi: 10.1097/MD.0000000000019651. PMID: 32221091 Free PMC Article

Reappraisal of morphological and immunohistochemical spectrum of intracranial and spinal solitary fibrous tumors/hemangiopericytomas with impact on long-term follow-up.

Shukla P, Gulwani HV, Kaur S, Shanmugasundaram D
Indian J Cancer 2018 Jul-Sep;55(3):214-221. doi: 10.4103/ijc.IJC_631_17. PMID: 30693881

Clinical outcomes of intracranial solitary fibrous tumor and hemangiopericytoma: analysis according to the 2016 WHO classification of central nervous system tumors.

Kim BS, Kim Y, Kong DS, Nam DH, Lee JI, Suh YL, Seol HJ
J Neurosurg 2018 Dec 1;129(6):1384-1396. doi: 10.3171/2017.7.JNS171226. PMID: 29372881

See all (10)