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Abnormal circulating dehydroepiandrosterone concentration

MedGen UID:
1389721
Concept ID:
C4477081
Finding
Synonyms: Abnormal serum androstenolone level; Abnormal serum dehydroepiandrosterone level; Abnormal serum DHEA
 
HPO: HP:0500022

Definition

A deviation from the normal concentration of dehydroepiandrosterone in the circulation. [from HPO]

Professional guidelines

PubMed

Saenger P, Klonari Z, Black SM, Compagnone N, Mellon SH, Fleischer A, Abrams CA, Shackelton CH, Miller WL
J Clin Endocrinol Metab 1995 Jan;80(1):200-5. doi: 10.1210/jcem.80.1.7829612. PMID: 7829612

Recent clinical studies

Etiology

Geyer J, Bakhaus K, Bernhardt R, Blaschka C, Dezhkam Y, Fietz D, Grosser G, Hartmann K, Hartmann MF, Neunzig J, Papadopoulos D, Sánchez-Guijo A, Scheiner-Bobis G, Schuler G, Shihan M, Wrenzycki C, Wudy SA, Bergmann M
J Steroid Biochem Mol Biol 2017 Sep;172:207-221. Epub 2016 Jul 5 doi: 10.1016/j.jsbmb.2016.07.002. PMID: 27392637
Utriainen P, Laakso S, Liimatta J, Jääskeläinen J, Voutilainen R
Horm Res Paediatr 2015;83(4):221-31. Epub 2015 Feb 7 doi: 10.1159/000369458. PMID: 25676474
Voutilainen R, Jääskeläinen J
J Steroid Biochem Mol Biol 2015 Jan;145:226-36. Epub 2014 Jun 9 doi: 10.1016/j.jsbmb.2014.06.004. PMID: 24923732
Fukui M, Kitagawa Y, Ose H, Hasegawa G, Yoshikawa T, Nakamura N
Curr Diabetes Rev 2007 Feb;3(1):25-31. doi: 10.2174/157339907779802094. PMID: 18220653
Wu FC, von Eckardstein A
Endocr Rev 2003 Apr;24(2):183-217. doi: 10.1210/er.2001-0025. PMID: 12700179

Diagnosis

Kostakis EK, Gkioni LN, Macut D, Mastorakos G
Front Horm Res 2019;53:135-161. Epub 2019 Sep 9 doi: 10.1159/000494909. PMID: 31499509
Utriainen P, Laakso S, Liimatta J, Jääskeläinen J, Voutilainen R
Horm Res Paediatr 2015;83(4):221-31. Epub 2015 Feb 7 doi: 10.1159/000369458. PMID: 25676474
Voutilainen R, Jääskeläinen J
J Steroid Biochem Mol Biol 2015 Jan;145:226-36. Epub 2014 Jun 9 doi: 10.1016/j.jsbmb.2014.06.004. PMID: 24923732
Karbowska J, Kochan Z
Horm Mol Biol Clin Investig 2013 Aug;14(2):65-74. doi: 10.1515/hmbci-2013-0009. PMID: 25436721
Saenger P, Klonari Z, Black SM, Compagnone N, Mellon SH, Fleischer A, Abrams CA, Shackelton CH, Miller WL
J Clin Endocrinol Metab 1995 Jan;80(1):200-5. doi: 10.1210/jcem.80.1.7829612. PMID: 7829612

Therapy

Tennilä J, Jääskeläinen J, Utriainen P, Voutilainen R, Häkkinen M, Auriola S, Morin-Papunen L, Liimatta J
J Clin Endocrinol Metab 2021 Aug 18;106(9):e3335-e3345. doi: 10.1210/clinem/dgab385. PMID: 34060603Free PMC Article
Maninger N, Wolkowitz OM, Reus VI, Epel ES, Mellon SH
Front Neuroendocrinol 2009 Jan;30(1):65-91. Epub 2008 Dec 3 doi: 10.1016/j.yfrne.2008.11.002. PMID: 19063914Free PMC Article
Fukui M, Kitagawa Y, Ose H, Hasegawa G, Yoshikawa T, Nakamura N
Curr Diabetes Rev 2007 Feb;3(1):25-31. doi: 10.2174/157339907779802094. PMID: 18220653
Wu FC, von Eckardstein A
Endocr Rev 2003 Apr;24(2):183-217. doi: 10.1210/er.2001-0025. PMID: 12700179
Ibáñez L, Potau N, Marcos MV, de Zegher F
J Clin Endocrinol Metab 2000 Sep;85(9):3251-5. doi: 10.1210/jcem.85.9.6814. PMID: 10999817

Prognosis

Tennilä J, Jääskeläinen J, Utriainen P, Voutilainen R, Häkkinen M, Auriola S, Morin-Papunen L, Liimatta J
J Clin Endocrinol Metab 2021 Aug 18;106(9):e3335-e3345. doi: 10.1210/clinem/dgab385. PMID: 34060603Free PMC Article
Jankowska EA, Rozentryt P, Ponikowska B, Hartmann O, Kustrzycka-Kratochwil D, Reczuch K, Nowak J, Borodulin-Nadzieja L, Polonski L, Banasiak W, Poole-Wilson PA, Anker SD, Ponikowski P
JAMA 2009 May 13;301(18):1892-901. doi: 10.1001/jama.2009.639. PMID: 19436016
Rodriguez A, Muller DC, Metter EJ, Maggio M, Harman SM, Blackman MR, Andres R
J Clin Endocrinol Metab 2007 Sep;92(9):3568-72. Epub 2007 Jun 26 doi: 10.1210/jc.2006-2764. PMID: 17595254

Clinical prediction guides

Jankowska EA, Rozentryt P, Ponikowska B, Hartmann O, Kustrzycka-Kratochwil D, Reczuch K, Nowak J, Borodulin-Nadzieja L, Polonski L, Banasiak W, Poole-Wilson PA, Anker SD, Ponikowski P
JAMA 2009 May 13;301(18):1892-901. doi: 10.1001/jama.2009.639. PMID: 19436016
Rodriguez A, Muller DC, Metter EJ, Maggio M, Harman SM, Blackman MR, Andres R
J Clin Endocrinol Metab 2007 Sep;92(9):3568-72. Epub 2007 Jun 26 doi: 10.1210/jc.2006-2764. PMID: 17595254
Khoromi S, Muniyappa R, Nackers L, Gray N, Baldwin H, Wong KA, Matheny LA, Moquin B, Rainer A, Hill S, Remaley A, Johnson LL, Max MB, Blackman MR
J Clin Endocrinol Metab 2006 Nov;91(11):4313-8. Epub 2006 Aug 15 doi: 10.1210/jc.2006-1122. PMID: 16912126
Wu FC, von Eckardstein A
Endocr Rev 2003 Apr;24(2):183-217. doi: 10.1210/er.2001-0025. PMID: 12700179
Buyalos RP, Jackson RV, Grice GI, Hockings GI, Torpy DJ, Fox LM, Boots LR, Azziz R
J Clin Endocrinol Metab 1998 Sep;83(9):3219-24. doi: 10.1210/jcem.83.9.5078. PMID: 9745431

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